INTRODUCTION Scimitar Syndrome is a relatively rare variety of partial anomalous pulmonary venous connection in which the right pulmonary veins form an anomalous confluence which drains into the infra-diaphragmatic inferior vena cava. The X-ray chest in these patients shows the typical Scimitar Sign. CASE REPORT We are presenting a patient who was diagnosed to have Scimitar Syndrome on the ba...

Scimitar syndrome is a rare congenital disorder with an incidence of approximately 2 per 100 000 live births.1 The hallmark of this syndrome is partial or complete anomalous venous return from the right lung, directly into the inferior vena cava (IVC), thereby creating a left-to-right shunt.2 The syndrome is almost invariably associated with other cardiac and extracardiac abnormalities includin...

Scimitar syndrome or pulmonary venolobar syndrome is a rare, complex, and variable malformation of the right lung characterized by an abnormal right sided pulmonary drainage into the inferior vena cava, malformation of the right lung, abnormal arterial supply, and sometimes cardiac malformation. Despite the varying degrees of pulmonary hypoplasia and pulmonary artery hypertension, about half of...

Clinical reasoning: the scimitar syndrome, due to the anomalous right pulmonary vein drainage, is clinically manifested as a simple atrial septal defect, with the described classic signs, few symptoms, ejection murmur in the pulmonary area, splitting of the second heart sound and right ventricular diastolic overload on the electrocardiogram. The scimitar sign on the chest X‐ray easily character...

Seven patients with scimitar syndrome underwent retrospective clinical and echocardiographic examination. The findings were: respiratory infection with dyspnea on moderate exercise in 90%, scimitar sign in four (57%), dextrocardia in five (71%), and interatrial septal defect in five (71%), one of whom had patent ductus arteriosus. Overall, two patients had patent ductus arteriosus: one also had...

80 Background --Scimitar syndrome, which presents with an anomalous right pulmonary vein that drains part or the entire right lung into the inferior vena cava (IVC) as its hallmark, is a rare association of congenital cardiopulmonary anomalies with an incidence of approximately 1 to 3 per 100,000 live births worldwide. It commonly presents with symptoms of respiratory distress and has an over-a...

Scimitar syndrome is a relatively uncommon constellation of cardio-pulmonary anomalies, its typical feature being partial anomalous pulmonary venous connection. It can present in the neonatal period as well as later in life. We present the case of a girl diagnosed in the newborn period, along with a brief review of literature.

The classic definition of the scimitar syndrome is a triad of hypoplasia of the right lung with anomalous venous drainage and a systemic arterial supply of a variable degree. We report a case in which a scimitar-shaped anomalous vein was observed on the plain chest radiograph, but subsequently a pulmonary angiogram showed that it drained normally into the left atrium.

An asymptomatic 40-year-old female was referred for preoperative clearance for gynecological surgery. The patient’s routine preoperative electrocardiogram (EKG) (Fig. 1) and chest x-ray (Fig. 2) were abnormal and for this reason the patient was referred for preoperative cardiac evaluation. Physical examination was significant for a prominent pulmonic component (P2) of the second heart sound (S2...