Quadricuspid aortic valve is a rare congenital malformation of the heart leading to significant aortic regurgitation or stenosis. Its diagnosis by transthoracic echocardiography is difficult. Most of the cases are diagnosed during surgery or autopsy. Associated abnormalities of the coronary arteries should also be searched, since surgical injury may have devastating results. We herein present a...

Quadricuspid aortic valves are rare congenital anomalies which can be diagnosed by various imaging modalities. Described is the case of a 77 year old female with a quadricuspid aortic valve diagnosed by cardiac CT.

quadricuspid aortic valve (qav) is an uncommon congenital anomaly which was an incidental finding during surgery or autopsy in the past. we present the case of a 44-year-old woman with moderately severe aortic regurgitation due to unequal cusp size qav diagnosed via transesophageal echocardiography. due to echocardiographic imaging improvement, the diagnosis of qav is now easier and earlier tha...

Congenital quadricuspid aortic valve (QAV) is a rare cardiac anomaly. Several different anatomical variations of a quadricuspid aortic valve have been described. Aortic regurgitation is the predominant valvular dysfunction associated with QAV and patients tend to present in their 5(th) or 6(th) decade of life. This anomaly is rarely picked up by transthoracic echocardiogram (TTE). A comprehensi...

Quadricuspid aortic valve is rare, with an estimated incidence of 0.008% to 1.46%. Most cases are encountered incidentally during aortic valve surgery or autopsy. The condition frequently progresses to aortic regurgitation, which can manifest in adulthood and may require surgical treatment. This anomaly may sometimes be associated with other malformations, the most common being coronary artery ...

Unicuspid aortic valve was first described more than half a century ago (Edwards, 1958). Although reported infrequently, the natural history of unicuspid aortic valve is poorly understood. Developmental abnormalities of aortic valve cusps in decreasing order of frequency include bicuspid (0.9%-1.3%), unicuspid (0.02%), quadricuspid (0.008%0.043%), and pentacupsid aortic valves (Cemri, 2000). De...

A 57-year-old woman presented with a history of dyspnea on exertion since 4 months prior to admission. She denied chest pain. Her medical history was not significant. Physical examination revealed wide pulse pressure and arterial hypertension (170/65 mmHg). A diastolic murmur of grade 4/6 was heard at the left sternal border. ECG displayed sinus rhythm with evidence of left ventricular enlargem...

Occurrence of quadricuspid aortic valves has been reported in humans, in nine dogs and in a greater white-toothed shrew. Moreover, two cases of developing aortic valves with four anticipated leaflets have been described in Syrian hamster embryos. Currently, however, no case of quadricuspid aortic valve in adult hamsters has been recorded. The aim here is to present four adults of this rodent sp...

Quadricuspid aortic valve (QAV) is a rare congenital cardiac entity. The recognition of QAV has clinical significance because QAV causes aortic valve dysfunction, commonly aortic regurgitation. QAV is often associated with other congenital cardiac abnormalities. Our case represents, to the best of our knowledge, the first reported case of QAV with a non-obstructive sub-aortic membrane.