The purpose of this paper is to report the occurrence of odontogenic keratocysts in a young child. Odontogenic keratocysts are one of the principal features of nevoid basal cell carcinoma syndrome. Their occurrence in this syndrome is usually during the second or third decades of life. This report describes the occurrence of odontogenic keratocysts in a 5-year-old, which proved to be the initia...

Sir, A 13-year-old girl presented with complaints of a boggy mass on her left frontoparietal scalp since birth with thinning of the overlying hair. The lesion was first noticed at birth and gradually increased in size with age. On examination, a large (12 × 14 cm) soft to firm, bosselated, skin-colored plaque was seen involving the vertex and left frontoparietal scalp. The surface was irregular...

BACKGROUND AND PURPOSE Medulloblastoma is one of the most common posterior fossa tumors to occur in children. Our purpose was to document the frequency, location, and time of occurrence of intracranial calcifications in cranial CT studies of children with medulloblastoma. METHODS We retrospectively reviewed cranial CT studies of 56 patients diagnosed with medulloblastoma from 1983 through 199...

Citation: Navarro-Navarro I, Ortiz-Prieto A, Gallo-Pineda G, Viedma-Martínez M, Jiménez-Gallo D, Linares-Barrios M. Acquired Bilateral Nevoid Telangiectasia Induced by Tamoxifen. Dermatol Pract Concept. 2023;13(2):e2023071. DOI: https://doi.org/10.5826/dpc.1302a71

nevoid basal cell carcinoma syndrome (bcns) is an autosomal dominant inherited disorder. multiple organ systems may be affected in this syndrome including abnormalities of the skin, skeletal system, genitourinary system and central nevus system. in this report, we present a case of nevoid basal cell carcinoma syndrome in a 26-year-old male patient. the patient had multiple odontogenic keratocys...

Unilateral nevoid telangiectasia is a rare vascular dermatosis, characterized by areas of superficial telangiectases distributed in a linear unilateral pattern. It was described in 1899 by Zeisler and Blascko. Several theories where developed in order to explain its etiopathogenesis. The most widely accepted is the one which establishes its probable association with an increase in the estrogen ...

FIG. 1 Linear and Whorled Nevoid Hypermelanosis: Linear and whorled hyperpigmented macules in a reticulate pattern along the Blaschko’s lines over trunk and limbs. A two-years-old boy presented with abnormal body pigmentation and body asymmetry noted since birth. A preceding vesicular eruption was absent. He was developmentally normal. Family history was insignificant. Examination revealed line...

OBJECTIVES PTCH, the human homologue of the Drosophila segment polarity gene, patched, has been identified as the gene responsible for nevoid basal cell carcinoma syndrome. The aim of this study was to investigate PTCH gene mutation in Chinese patients with nevoid basal cell carcinoma syndrome. MATERIALS AND METHODS DNA was isolated from both odontogenic keratocyst tissue and peripheral blood...