نتایج جستجو برای: myo15a

تعداد نتایج: 60  

2015
Nazir Ahmad Muhammad Zubair M. Ahmed Sheikh Riazuddin

Deafness is inherited most commonly following autosomal recessive mode of inheritance as isolated clinical finding .Genetic and clinical heterogeneity of disorder prevent pooling of affected families and is a big barrier in gene mapping by conventional techniques. However, because of consanguinity, linkage analysis can be used to find disease causing loci /genes in small nuclear families. This ...

Journal: :Human molecular genetics 1996
K A Brown A H Janjua G Karbani G Parry A Noble G Crockford D T Bishop V E Newton A F Markham R F Mueller

Autosomal recessive non-syndromal hearing impairment (NSRD) is genetically heterogeneous. Five loci have been identified to date which map to chromosomes 13 (DFNB1), 11 (DFNB2), 17 (DFNB3), 7 (DFNB4) and 14 (DFBN5). We report definite linkage of NSRD to the locus DFNB1 in a single family of 27 families studied of Pakistani origin. Haplotype analysis of markers in the pericentromeric region of c...

Journal: :Journal of medical genetics 1995
S Winata I N Arhya S Moeljopawiro J T Hinnant Y Liang T B Friedman J H Asher

Bengkala is an Indonesian village located on the north shore of Bali that has existed for over 700 years. Currently, 2.2% of the 2185 people in this village have profound congenital deafness. In response to the high incidence of deafness, the people of Bengkala have developed a village specific sign language which is used by many of the hearing and deaf people. Deafness in Bengkala is congenita...

2015
Fatima Ammar-Khodja Crystel Bonnet Malika Dahmani Sofiane Ouhab Gaelle M Lefèvre Hassina Ibrahim Jean-Pierre Hardelin Dominique Weil Malek Louha Christine Petit

The genetic heterogeneity of congenital hearing disorders makes molecular diagnosis expensive and time-consuming using conventional techniques such as Sanger sequencing of DNA. In order to design an appropriate strategy of molecular diagnosis in the Algerian population, we explored the diversity of the involved mutations by studying 65 families affected by autosomal recessive forms of nonsyndro...

Journal: :Investigative ophthalmology & visual science 2018
Tengyang Sun Ke Xu Yanfan Ren Yue Xie Xiaohui Zhang Lu Tian Yang Li

Purpose Usher syndrome (USH) refers to a group of autosomal recessive disorders causing deafness and blindness. The objectives of this study were to determine the mutation spectrum in a cohort of Chinese patients with USH and to describe the clinical features of the patients with mutations. Methods A total of 119 probands who were clinically diagnosed with USH were recruited for genetic analy...

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