نتایج جستجو برای: hspb1

تعداد نتایج: 443  

2018
Lu Liu Dandan An Junying Xu Bin Shao Xing Li Jing Shi

Citation: Liu L, An D, Xu J, Shao B, Li X and Shi J (2018) Ac2-26 Induces IKKβ Degradation Through Chaperone-Mediated Autophagy Via HSPB1 in NCM-Treated Microglia. Front. Mol. Neurosci. 11:76. doi: 10.3389/fnmol.2018.00076 Annexin A1 (ANXA1) is an endogenous protein with potent anti-inflammatory properties in the brain. Although ANXA1 has been predominantly studied for its binding to formyl pep...

Journal: :Human molecular genetics 2006
Steven Ackerley Paul A James Arran Kalli Sarah French Kay E Davies Kevin Talbot

Distal hereditary motor neuronopathies (dHMNs) are a clinically and genetically heterogeneous group of disorders in which motor neurons selectively undergo age-dependant degeneration. Mutations in the small heat-shock protein HSPB1 (HSP27) are responsible for one form of dHMN. In this study, we have analysed the effect of expressing a form of mutant HSPB1 in primary neuronal cells in culture. M...

2016
Chan Chung Matthew J Elrick James M Dell'Orco Zhaohui S Qin Shanker Kalyana-Sundaram Arul M Chinnaiyan Vikram G Shakkottai Andrew P Lieberman

Selective neuronal vulnerability is characteristic of most degenerative disorders of the CNS, yet mechanisms underlying this phenomenon remain poorly characterized. Many forms of cerebellar degeneration exhibit an anterior-to-posterior gradient of Purkinje cell loss including Niemann-Pick type C1 (NPC) disease, a lysosomal storage disorder characterized by progressive neurological deficits that...

2011
Leonardo Almeida-Souza Vincent Timmerman Sophie Janssens

The special architecture of neurons in the peripheral nervous system, with axons extending for long distances, represents a major challenge for the intracellular transport system. Two recent studies show that mutations in the small heat shock protein HSPB1, which cause an axonal type of Charcot-Marie-Tooth (CMT) neuropathy, affect microtubule dynamics and impede axonal transport. Intriguingly, ...

2017
Laura Hoffman Christopher C. Jensen Masaaki Yoshigi Mary Beckerle

Despite the importance of a cell's ability to sense and respond to mechanical force, the molecular mechanisms by which physical cues are converted to cell-instructive chemical information to influence cell behaviors remain to be elucidated. Exposure of cultured fibroblasts to uniaxial cyclic stretch results in an actin stress fiber reinforcement response that stabilizes the actin cytoskeleton. ...

Background: Molecular marker based cancer diagnosis gaining more attention in the current genomics era. So, Hspb1 and Tp53 gene characterization and their mRNA expression might be helpful in diagnosis andprognosis ofcat mammary adenocarcinoma. It will also add informationin comparative cancer genetics and genomics. Objectives: Eight tumors of Siamese cats were analyzed to ascertain germ-line an...

2016
Malek Kammoun Brigitte Picard Thierry Astruc Mohammed Gagaoua Denise Aubert Muriel Bonnet Véronique Blanquet Isabelle Cassar-Malek

Even though abundance of Hsp27 is the highest in skeletal muscle, the relationships between the expression of HspB1 (encoding Hsp27) and muscle characteristics are not fully understood. In this study, we have analysed the effect of Hsp27 inactivation on mouse development and phenotype. We generated a mouse strain devoid of Hsp27 protein by homologous recombination of the HspB1 gene. The HspB1-/...

2016
He-Xiao Wang Yang Yang Hao Guo Dian-Dong Hou Song Zheng Yu-Xiao Hong Yun-Fei Cai Wei Huo Rui-Qun Qi Li Zhang Hong-Duo Chen Xing-Hua Gao

Hyperthermia has shown clinical potency as a single agent or as adjuvant to other therapies in cancer treatment. However, thermotolerance induced by thermosensitive genes such as the heat shock proteins can limit the efficacy of hyperthermic treatment. In the present study, we identified HSPB1 (HSP27) is hyperthermically inducible or endogenously highly expressed in both murine and human melano...

Journal: :Brain : a journal of neurology 2008
Ines Dierick Jonathan Baets Joy Irobi An Jacobs Els De Vriendt Tine Deconinck Luciano Merlini Peter Van den Bergh Vedrana Milic Rasic Wim Robberecht Dirk Fischer Raul Juntas Morales Zoran Mitrovic Pavel Seeman Radim Mazanec Andrzej Kochanski Albena Jordanova Michaela Auer-Grumbach A T J M Helderman-van den Enden John H J Wokke Eva Nelis Peter De Jonghe Vincent Timmerman

Distal hereditary motor neuropathy (HMN) is a clinically and genetically heterogeneous group of disorders affecting spinal alpha-motor neurons. Since 2001, mutations in six different genes have been identified for autosomal dominant distal HMN; glycyl-tRNA synthetase (GARS), dynactin 1 (DCTN1), small heat shock 27 kDa protein 1 (HSPB1), small heat shock 22 kDa protein 8 (HSPB8), Berardinelli-Se...

2015
Małgorzata Żychowska Zbigniew Jastrzębski Grzegorz Chruściński Monika Michałowska–Sawczyn Alicja Nowak-Zaleska

BACKGROUND Overexpression of HSPA1A and HSPB1 has been shown to indicate stress and the degradation of damaged proteins. Therefore, the expression of these genes is often evaluated during exercise. Vitamin supplementation in young athletes may affect the expression of these genes, and help to maintain health and improve the effects of training. METHODS Fourteen top junior female athletes (age...

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