Uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis is a rare congenital anomaly of the Müllerian duct system referred to as Herlyn-Werner-Wunderlich syndrome. Because of its rare occurrence, a high level of suspicion is often required for diagnosis. Clinically, these patients usually present after menarche with pelvic pain, dysmenorrhea, and a palpable pelvic mass. We p...

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of mullerian duct anomalies characterized by the triad uterine didelphys, obstructed hemivagina and ipsilateral renal agenesis. We report two cases HWW in young women with abdominal pain. This diagnosis can easily be missed if clinician not aware syndrome. In one case, computed tomography image hematocolpos was initially mistaken for cys...

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital abnormality of the female urogenital tract. We reported OHVIRA syndrome in a 15-year-old girl, who was referred to King Faisal Specialist Hospital and Research Centre, due to hematocolpos and an imperforate hymen. The patient was diagnosed as having an absent right kidney since childhood. She presented wi...

Acute urinary retention is unusual in children and is usually a candidate for visiting the emergency department upon initial discovery. We report a 12-year-old girl who complained of acute urinary retention. Ultrasonography demonstrated a large echogenic mass over the vagina and mild dilation of the uterus. Imperforate hymen associated with hematocolpos and hematometrium was diagnosed. Cruciate...

Obstructed hemi-vagina and ipsilateral renal agenesis (OHVIRA) syndrome is a complex of Müllerian Wolffian duct anomalies constituted by obstructed that may form hematocolpos with anomaly different degrees didelphic uterine anomalies. Due to the obstructive reproductive tract, endometriosis differing severities be common complication OHVIRA syndrome. Here, we report three women showed clinical ...

Background: Patients with a transverse vaginal septum generally present at the age of menarche with complain of cyclic pelvic or abdominal pain due to retention of blood above the obstruction. In the absence of menstruation this women did not have typical hematocolpos. Materials and Methods: A rare case of hypothalamic amenorrhea and transverse vaginal septum were reported. A 28- year-old woman...

Background: Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of Mullerian duct anomalies. The characteristic triad this includes didelphys uterus, obstructed hemivagina, and ipsilateral renal agenesis, recently known as Obstructed Hemivagina Ipsilateral Renal Anomaly (OHVIRA) syndrome. most common presentation abdominal pelvic pain, dysmenorrhea, mass secondary to hematocolpos, hematos...