factor x deficiency

BACKGROUND Autosomal recessive bleeding disorders (ARBDs) include deficiencies of clotting factors I, II, V, VII, X, XI, XIII, vitamin K dependent clotting factors, combined factor V & VIII, Von Willebrand Disease (vWD) type 3, Glanzmann's thrombasthenia (GT) and Bernard-Soulier syndrome. Patients with primary bleeding disorders from all the major provincial capitals of Pakistan were screened f...

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long term follow up study on a large group of patients with congenital factor xiii deficiency treated prophylactically with fibrogammin p®

Journal: :iranian journal of pharmaceutical research 0

majid naderi genetic research center in non-communicable disease, zahedan university of medical sciences mehran karimi hematology research center, shiraz university of medicalsciences, shiraz, iran maryam sadat hosseini department of hematology, allied medical school, tehran university of medical sciences, tehran, iran eshagh moradi affiliation mortea shamsizadeh affiliation akbar dorgalaleh department of hematology, allied medical school, tehran university of medical sciences, tehran, iran

factor xiii deficiency (fxiiid) is an extremely rare hemorrhagic disorder with a prevalence of 1/3-5 million. management of disease is performed by fresh frozen plasma (ffp), cryoprecipitate (cp) or fxiii concentrate (fibrogammin p®). our objective was to assess safety and effectiveness of fibrogammin p® in patients with fxiiid. for this purpose we designed this long-term follow up study on a l...

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