Burch (1936), in a comprehensive review, was largely responsible for furthering recognition of the condition in America, and the number of cases that have been reported, mostly in the ophthalmological literature, during the past ten years is an indication that arachnodactyly is not of extreme rarity, and that many milder cases and 'formes frustes ' have previously passed unrecognized. Stewart (...

Introduction: Ectopia cordis is a rare congenital defect and a true neonatal surgical emergency, with an occurrence of 5.5 to 7.9 cases per million live births [1]. This impressive malformation develops due to failure of maturation of the midline mesodermal components of the chest and abdomen [2]. The disorder is classified into five anatomical types including cervical, cervicothoracic, thoraci...

Ectopia cordis is derived from two Latin words which means outside and heart [1]. It is a rare congenital malformation in which the heart is formed outside the thoracic cavity. It occurs in 1 in 5-7 per 1,000,000 live births [2]. It may occur as an isolated defect or in association with other body wall defects that affect the thorax, abdomen or both [3]. It may also be associated with other int...

Amniotic band syndrome is a collection of fetal malformations associated with fibrous bands that appear to entangle or entrap various fetal parts in utero leading to deformation, malformation, or disruption. Ectopia cordis is a rare congenital defect in fusion of the anterior chest wall resulting in extrathoracic location of the heart. In this article, we report a rare case of ectopia cordis an...