ABSTRACT Background: Congenital malformations of lung, such as congenital lobar emphysema, cystic adenomatoid malformation, bronchial cyst, pulmonary sequestration are rare occurrence. However, our hospital being in a rural area attracts large number patients with complex malformations. Method: This retrospective analysis is done to evaluate diagnostic accuracy, safety and efficacy outcomes ope...

background the most common space occupying lesions of the fetal thorax are congenital diaphragmatic hernia (cdh), congenital cystic adenomatoid malformation (ccam), and bronchopulmonary sequestration (bps). although applications of prenatal mri have been vastly improved in the recent years, its use in the assessment of space occupying lesions of the fetal chest differs among centers. objectives...

Congenital cystic adenomatoid malformation is a rare, but well-known disease. It can be managed conservatively in patients without symptoms or require surgical removal when symptomatic. The surgical option of choice is en bloc resection of the affected lesion. We report an experience of life-threatening congenital cystic adenoid malformation in a low-birth-weight (1,590 g) premature neonate who...

Congenital cystic adenomatoid malformation (CCAM) is a rare bronchopulmonary malformation characterized by loss of the normal pulmonary tissue. CCAM may be frequently associated with cardiac and renal anomalies. Rarely, CCAM may be seen with chromosome abnormalities. This is the first reported neonatal case of prenatally detected CCAM and postnatally diagnosed trisomy 13.

Pediatric respiratory disease related to congenital and genetic etiologies are important topics found on the USMLE. Congenital disease to be aware of include Diaphragmatic hernias, congenital cystic adenomatoid malformation, surfactant deficiency, pediatric pulmonary hypoplasia, and bronchopulmonary dysplasia. Genetic disease to be aware of include cystic fibrosis, alpha 1 antitrypsin, and prim...

background congenital pulmonary lesions may be diagnosed through ultrasonographic screenings or be revealed as causes of respiratory distress in the neonatal period and infancy. less commonly, they are detected as incidental features. objectives our study represents the diversity of congenital pulmonary lesions and their characteristics during an 11-year period in a referral teaching children’s...

Congenital pulmonary airway malformation (CPAM), previously known as congenital cystic adenomatoid malformation (CCAM), is an inborn abnormality of the lower respiratory system. Most often diagnosed in the perinatal period, these anomalies usually present with tachypnea, cyanosis, and respiratory distress. However, rare cases are asymptomatic and undiagnosed until adulthood.

Congenital Cystic Adenomatoid Malformation (CCAM) is a rare development abnormality of the lung occurring in 14 / 100,000 live birth.it is often confused with pneumatocoele or pneumothorax which are common in developing countries. We report here a case of 5 months old baby with features of respiratory distress since birth and CECT thorax suggestive of large cystic lesion of left lung i.e., CCAM.

Pediatric respiratory disease related to congenital and genetic etiologies are important topics found on the USMLE. Congenital disease to be aware of include Diaphragmatic hernias, congenital cystic adenomatoid malformation, surfactant deficiency, pediatric pulmonary hypoplasia, and bronchopulmonary dysplasia. Genetic disease to be aware of include cystic fibrosis, alpha 1 antitrypsin, and prim...