Congenital lobar emphysema is a rare variety of congenital malformation of lung characterized by over distension of a lobe of the lung due to partial obstruction of the bronchus. It is one of the rare causes of infantile respiratory distress requiring surgical resection of affected lobe. We are reporting the case of an 8-week-old baby who presented with respiratory distress related to CLE affec...

The term congenital lobar emphysema was used by Robertson and James (1951) to denote infantile emphysema when pulmonary infection or intrabronchial foreign bodies are absent. Although in most instances only one lobe is affected, a few patients have emphysema of more than one lobe or subsequently develop emphysema of a second lobe (Kernan, 1944; Ehrenhaft and Taber, 1953; Sloan, 1953; Potts, Hol...

Congenital lobar emphysema (CLE) is a rare congenital abnormality characterized by over inflation of a pulmonary lobe. It often presents a diagnostic and therapeutic dilemma. No case has been described in Uganda in the previous 10 years. We describe a case of a 2 months old infant who presented with severe respiratory distress. A diagnosis of congenital left upper lobar emphysema was establishe...

Congenital lobar emphysema (CLE) is a rare developmental malformation that presents as neonatal respiratory distress and can be successfully managed with prompt intervention. Hyperinflation of the affected lobe mediastinal shift characteristic radiological finding. However, etiology mostly remains unknown. Here, we report case CLE microscopically revealed bronchial cartilaginous hypoplasia an u...