Congenital Cystic Adenomatoid Malformation (CCAM) is a rare development abnormality of the lung occurring in 14 / 100,000 live birth.it is often confused with pneumatocoele or pneumothorax which are common in developing countries. We report here a case of 5 months old baby with features of respiratory distress since birth and CECT thorax suggestive of large cystic lesion of left lung i.e., CCAM.

In recent years the diagnosis of congenital cystic disease of the lung has been clarified and restricted as a result of the recognition of a variety of emphysematous and cystic lesions of diverse etiologies. True cystic disease is rare.1 Rarer still is the closely related condition first reported in 1897 by Stoerk as " cystic fetal bronchial adenoma, " 2 and introduced in the English language m...

Congenital cystic adenomatoid malformation (CCAM) of the lung is an uncommon congenital anomaly, especially in young adults. This study reports an 18-yr-old male with CCAM involving the right upper lobe, who presented with a moderate spontaneous haemopneumothorax initially. The patient also had bilateral abdominal cryptorchidism which required surgical treatment earlier in childhood. The chest ...

Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare pulmonary lesion. The prognosis is variable ranging from perinatal death to spontaneous in utero regression, with no neonatal morbidity. We present a case of CCAM diagnosed at 23 weeks' gestation using results of prenatal sonograms. Both prenatal Two-Dimensional and Three-Dimensional sonograms revealed multiple cystic lesio...

Congenital cystic adenomatous malformations (CCAMs) of the lung represent the most common lung defect diagnosed prenatally. CCAMs are intrapulmonary lesions with a typical hyperechoic appearance on ultrasound (US), with or without cystic components. Both sides of the lung, both sexes, and all races are equally affected. Most fetuses with CCAM are detected prenatally and have a good outcome, but...

Ultrastructural study of a congenital cystic adenomatoid malformation of the lung revealed a persistence of type 2 pneumocytes lining the alveolar and gland-like spaces. The larger cystic areas were lined by normal bronchiolar-type epithelium and were surrounded by a few smooth muscle cells. The interstitium contained undifferentiated mesenchymal cells. No cartilage or bronchial glands were pre...

Patients with congenital lung cysts are at increased risk of developing carcinoma, but the mechanisms concerned are not clear. The case of a young adult who developed a bronchioloalveolar carcinoma associated with a cystic congenital adenomatoid malformation is reported. The adjacent lung showed an unusual intra-alveolar hyperplasia of mucous cells. Two further cases of congenital adenomatoid m...

Congenital cystic adenomatoid malformation of the bronchi with bilateral lung involvement has only previously been reported in one possible adult case. This report describes a young man with bilateral diffuse lung involvement, characteristic histological features, and a mixed restrictive/obstructive lung function pattern.

UNLABELLED Congenital cystic adenomatoid malformation (CCAM), also named congenital pulmonary airway malformation (CPAM), is a congenital abnormality of lung which is uncommon in adults. Here we present 2 adult cases of CCAM with unusual clinical and pathologic findings. One case was complicated with aspergillosis which was seldom reported. The other case was suffered bilateral lesions and the ...

INTRODUCTION Thoracoscopic lobectomy for congenital pulmonary airway malformation has been indicated from the neonatal period to adolescence. However, it is difficult to approach the pulmonary artery for lobectomy in congenital lung malformations with incomplete or absent interlobar fissures. Multidetector computed tomographic images and computed tomography pulmonary angiography gave us helpful...