isolated impacted supernumerary teeth are quite rare, but they can be seen associated with several syndromes such as cleidocranial dysostosis or gardner's syndrome. this article aims to discuss a case of sequential formation of supernumerary teeth with no other associated disease or syndrome. a 17-year-old iranian male with 8 impacted supernumerary teeth was referred to the department of pediat...

OBJECTIVE To describe a rare case of cleidocranial dysplasia, an autosomal dominant inherited disease involving the skeleton and teeth, with delayed diagnosis. CASE REPORT We report a 24-year-old man with cleidocranial dysplasia admitted with hearing loss, rhinolalia, dyspnea and fatigue. Partial absence of clavicles, a bell-shaped ribcage, an open frontal fontanel, unerupted permanent teeth ...

Cleidocranial dysplasia is an extremely rare familial disorder characterized by partial or complete absence of clavicles, characteristic craniofacial deformities, and the presence of numerous supernumerary and unerupted teeth. Here, the author reviews the striking radiographic findings of cleidocranial dysplasia in a 16-year-old adolescent boy who presented with delayed teeth eruption.

Multiple supernumerary teeth affecting all four quadrants of the jaw are a rare dental anomaly which has become a chance finding on routine dental panoramic tomography (DPT). In this paper, two cases from the English-speaking Caribbean are reported. The role of radiography in the diagnosis and management of this rare developmental dental anomaly is emphasized. The paper stresses the importance ...

Indian Journal of Anaesthesia | Vol. 60 | Issue 10 | Oct 2016 782 Oral Med Oral Pathol Oral Radiol 2013;115:46‐55. 4. Bufalino A, Paranaíba LM, Gouvêa AF, Gueiros LA, Martelli‐Júnior H, Junior JJ, et al. Cleidocranial dysplasia: Oral features and genetic analysis of 11 patients. Oral Dis 2012;18:184‐90. 5. Almenrader N, Passariello M, Cascone P. Anaesthesia for a child with cleidocranial dyspla...

Cleidocranial dysplasia is an autosomal dominant heritable skeletal disorder. The characteristic features of cleidocranial dysplasia (CCD) may include hypoplasia of the clavicle, delayed closure of frontanelles, late tooth eruption, and other skeletal disorders. This case report describes clinical and radiographic manifestations at the age of 11 and 29 of a CCD patient, investigates the mutatio...

Cleidocranial dysostosis is a generalized skeletal dysplastic condition and primarily affects the development of the bones and teeth. The genetic etiology lies on chromosome number 6p21, core binding factor (CBFA1). This paper explains the treatment procedure carried out for a sixteen year old female patient diagnosed with cleidocranial dysostosis. Therapy includes surgical removal or exposure ...

Cleidocranial dysplasia or mutational dysostosis or cleidocranial dysostosis is a generalized skeletodental dysplastic disorder, inherited in an autosomal dominant pattern. The expression of this disorder can vary widely in severity, even within the same family. This is a relatively rare disease and has no standard effective treatment option as of yet. Here we present a case report of affected ...

The term Scheuthauer-Marie-Sainton syndrome is also known as cleidocranial dysplasia or dystosis and derived from ancient greek words cleido (collar bone), knanion (head) (abnormal formation). It an uncommon but well genetic skeletal condition autosomal dominant malformation affecting bones teeth. most common dental abnormalities in affected individuals are hypoplastic/ aplastic clavicles, open...