The Budd-Chiari syndrome is a heterogeneous group of disorders characterized by obstruction of hepatic venous outflow at any level from the small hepatic veins to the junction of the inferior vena cava with the right atrium. We present two cases of Budd- Chiari syndrome with severe ascites associated with polycythemia vera in first case and protein C deficiency in the second, in both cases tran...

The budd-Chiari syndrome is characterized by thrombotic or non thrombotic reduction of the venous hepatic flow. Several works have enabled the comprehension of budd-Chiari syndrome as well as the diagnosis and treatment. This clinical review attempted to present the budd-Chiari syndrome overall and more particularly the history, etiology, pathophysiology, diagnosis and the understanding of the ...

Résumé L’atteinte hépatique au cours de la sarcoïdose est une localisation fréquente, habituellement asymptomatique. La cholestase anictérique et l’hypertension portale représentent ses principales complications. Le syndrome de Budd-Chiari est une complication peu connue qui demeure exceptionnelle. Nous rapportons un nouveau cas de syndrome de Budd-Chiari compliquant une sarcoïdose hépatique ch...

INTRODUCTION Budd-Chiari syndrome is a very rare pathological entity that ultimately leads to liver failure. Several therapeutic modalities, including percutaneous transluminal angioplasty, have been attempted to save the life of patients with Budd-Chiari syndrome. Few reports have described a salvage living donor liver transplantation performed after percutaneous transluminal angioplasty in a ...

BACKGROUND Behçet's disease is a chronic inflammatory disease involving multiple systems, with vasculitis being the most important pathological feature. Multiple colon perforations are thought to be secondary to vasculitis and they occur in patients with ulcers. These may be encountered within the entire colon but most commonly in the ileocecal region. Intestinal perforation and Budd-Chiari syn...

There is increasing evidence that Budd Chiari syndrome occurs when acquired predisposing factor(s) affect a susceptible individual with one or more underlying thrombophilic conditions. Geographical variations in disease pattern of Budd Chiari syndrome exist, which may reflect differing predisposing factors. We review a change in disease profile of Budd Chiari syndrome in India over the past thr...

Transjugular intrahepatic portosystemic shunt (TIPS) is a new treatment modality in patients of intractable ascites with Budd-Chiari syndrome. We report a young lady who presented with intractable ascites and encephalopathy and diagnosed to have Budd-Chiari syndrome. She was treated with TIPS and on follow-up after 12 months she is free of ascites, encephalopathy and able to perform her daily w...

A patient with systemic lupus erythematosus was first diagnosed after she had developed the Budd-Chiari syndrome. We believe that the Budd-Chiari syndrome was part of her tendency for thrombosis, induced by the presence of a lupus anticoagulant. The association between enhanced thrombosis and the lupus anticoagulant is discussed, and the need for prompt recognition and administration of anticoa...

filling defects are often observed on 99mtc sulfur colloid liver scans. hot spots are much less frequently seen. superior vena cava syndrome is the most frequent cause of this finding. in this report 3 patients with s.v.c and budd - chiari syndrome with hot spot on liver scan are presented. mechanisms of scintigraphic patterns are reviewed.

Budd-Chiari syndrome is defined as hepatic venous outflow tract obstruction regardless of the level of the obstruction (anywhere between the small hepatic veins to the junction of the inferior vena cava and right atrium) or the cause of obstruction. It is frequently associated with hepatomegaly, abdominal pain, ascites and hepatic dysfunction, and patients with Budd-Chiari syndrome often demons...