the aim of this study was to assess the role of hla-b*27 and it’s subtypes in determining severity and clinical manifestations of ankylosing spondylitis (as). a total of 163 as patients were assessed for clinical manifestations and severity using structured questionnaires. hla-b*27 screening and b*27 sub-typing were performed by pcr. one hundred twenty two patients (74.8%) were b*27 positive. t...

background cerebral venous sinus thrombosis (cvst) is a frequent cause of cerebrovascular disease in iran. objectives in this study, we report cumulative data of published iranian studies in a systematic manner with critically appraisal and presenting future directions. materials and methods the authors systematically searched the isi web of knowledge, pubmed, scopus, ebesco and iranmedex for k...

background: irritable bowel syndrome (ibs) is one of the most prevalent gastrointestinal disorders which includes the majority section of general practitioners or gastroenterologists visits. the type or prevalence of clinical signs and symptoms of the syndrome may be different among males and females. we decided to assess and compare the frequency of different signs and symptoms of ibs in men a...

background and aim kindler syndrome is a subtype of epidermolysis bullosa with gingival fragility and periodontitis as common oral manifestations of these patients. because of the early onset and rapid progression of periodontitis in these patients, clinical management of their oral status is an important aspect of their multidisciplinary care and treatment case presentation we present a succes...

hemophagocytic syndrome (hps) is an uncommon manifestation in systemic lupus erythematosus (sle). clinical features of hps include fever, pancytopenia, abnormal liver enzyme, hepatosplenomegaly, lymphadenopathy, and coagulation disorder. hps comprises primary and reactive forms. herein, we describe a case of untreated sle with hps as one of the first manifestations of systemic lupus.

Background: Cerebral Salt Wasting Syndrome (CSWS) refers to the process of intracranial lesions, sodium salt loss by hypothalamus-renal pathway and caused clinical manifestations syndrome of high urinary sodium, hyponatremia, hypovolemia. The clinical manifestations and laboratory are similar to syndrome of inappropriate antidiuretic hormone secretion (SIADH). It is easy to be misdiagnosed. Cas...

Ovarian fibromas are the most common benign solid ovarian tumors, which preoperative diagnosis often is difficult. Ovarian fibromas, especially in bilateral cases, may be representative of Gorlin syndrome.Gorlin syndrome (GS) is a rare autosomal dominant disorder with predisposition to basal cell carcinomas (BCCs) and other various benign and malignant tumors. To report a case of a young patien...

how to cite this article: asadi-pooya aa, sharifzade m. west syndrome in south iran: electro-clinical manifestations. iran j child neurol. 2013 summer; 7(3): 40-44. objective we aimed to determine the clinical and electroencephalographic (eeg) characteristics of the patients with west syndrome (ws) in south iran. materials & methods in this retrospective study, all patients with a clinical diag...