نتایج جستجو برای: autosomal recessive

تعداد نتایج: 41260  

Journal: :Orphanet Journal of Rare Diseases 2006

Journal: :Journal of Clinical Pathology 1988

Backgrounds: Hypohidrotic ectodermal dysplasia (HED) is a rare genetic disorder, distinguished by hypotrichosis, hypohidrosis, and hypodontia. HDE can be inherited in X-linked recessive manner as a result of mutations in the ectodysplasin A (EDA) gene as well as autosomal dominant and autosomal recessive manners both of them caused by mutations in EDA receptor (EDAR) and EDAR-associated death d...

Journal: :Egyptian Journal of Health Care 2023

Phenylketonuria (PKU) is an autosomal recessive inborn error of phenylalanine metabolism resulting from deficiency hydroxylase (PAH).

Journal: :Journal of clinical images and medical case reports 2022

Chronic diarrhea, juvenile cataracts, and tendon xanthomas, among other neurological systemic disturbances, characterize Cerebrotendinous xanthomatosis, an autosomal recessive lipid storage disease

2004
NORIO OHBA SHINOBU WATANABE SHINGO FUJITA Norio Ohba

A sibship of a brother and sister with congenital bilateral pseudoglioma is described. The most prominent abnormality was a greyish-white vascularised mass in the retrolental spaces, which was noted as early as the first weeks of life. Corneal opacities, posterior synechiae, and complicated cataracts developed within 1 to 2 years age. The sibship showed normal chromosomes and had no systemic di...

Journal: :Journal of Medical Genetics 1982

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