OBJECT Surgery for Chiari malformation Type I (CM-I) is one of the most common neurosurgical procedures performed in children, although there is clearly no consensus among practitioners about which surgical method is preferred. The objective of this meta-analysis was to compare the outcome of posterior fossa decompression with duraplasty (PFDD) and posterior fossa decompression without duraplas...

Seven in a thousand children are born with multiple malformations:' many of them will have one of the thousand or so malformation syndromes that have been described in the published reports. All malformation syndromes are rare and it is unlikely that the average clinician, or even the experienced dysmorphologist, will be able to recall all of them and to keep up to date with new reports. Nevert...

SPOndylar and NAsal changes, with STRIations of the Metaphyses (SPONASTRIME) dysplasia (SD) is a dwarfing autosomal recessive syndrome, characterized by a variety of clinical and radiographic features, which form the basis for diagnosis. We describe the presentation of an Arnold Chiari malformation in a patient with a clinical diagnosis of SD. The malformation was successfully treated by decomp...

Address for Correspondence: Dr. Joseph Abraham, Department of Anatomy, Government Medical College and Hospital, Chandigarh 32, India, 160030. Phone No.: +919041466127. E-Mail: [email protected] Chiari malformations (CM) are named for Hans Chiari, an Austrian pathologist, who first identified type I-III in 1891. This study was conducted on 400 fetuses obtained from department of Obstetrics an...

We report on the case of two young patients with type I Arnold-Chiari malformation (ACM), as revealed by a central sleep apnoea (CSA) syndrome without any other neurological defect. Case 1 was a 14-yr-old male patient, who developed severe alveolar hypoventilation and needed long-term mechanical ventilation via a tracheostomy. Case 2 was a 39-yr-old male patient, who developed features suggesti...

Neural tube defects of the brain and spinal cord, among the most common birth defects in the United States, cause neurologic morbidity from the lesions themselves and from associated hydrocephalus and Arnold-Chiari malformation. Because the myelomeningoceles, and encephaloceles are repaired surgically within hours of birth, neonatal anesthetic management with attention to fluids, body temperatu...

1. Manivel S, Prasad R, Jacob R. Anesthetic management of a child with Klippel-Feil syndrome in the radiology suite. Paediatr Anaesth. 2005;15:171--2. 2. Cakmakkaya OS, Kaya G, Altintas F, et al. Anesthetic management of a child with Arnold-Chiari malformation and Klippel-Feil syndrome. Paediatr Anaesth. 2006;16:355--6. 3. Subramanyam R, Cudilo EM, Hossain MM, et al. To pretreat or not to pretr...