Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) is a distinct group of systemic with severe multi-organ involvement. It includes three types: granulomatosis polyangiitis (GPA), eosinophilic (EGPA), and microscopic (MPA). Cutaneous manifestations are present at the time presentation in around 35% cases more frequently encountered EGPA than GPA or MPA. They can also occur ...