Anorectal malformations are congenital anomalies that form a spectrum of disorders, from the most benign type with excellent functional prognosis, to very complex, such as cloaca malformation in females in which the rectum, vagina and urethra fail to develop separately and instead drain via a single common channel into the perineum. The severity of this phenotype suggests that the defect occurs...

Müllerian duct anomalies are rare in the general population, occurring less than 3% of women, but much more prevalent female patients with anorectal malformation, up to 30% these patients. Unicornuate uterus a rudimentary non-communicating horn is congenital anomaly development which can be seen isolation or conjunction other anomalies, several case reports described VACTERL association. These ...

Two cases of bizarre skeletal anomalies associated with intestinal malformation are presented. One patient had ileal atresia and Hirschsprung's disease, and the other anorectal malformation. Abnormalities in the number and morphology of ribs and vertebrae were present. Esophageal atresia often is associated with skeletal abnormalities, including supernumerary ribs, but these usually are not sev...

Fecoflowmetry (FFM) has been introduced to simulate natural anorectal evacuation. So far, few reports have described the effect of the herbal medicine Daikenchuto (DKT) on impaired anorectal motor function. The aim of this pilot study was to assess anorectal motor function by FFM in postoperatively impaired patients with an anorectal malformation (ARM) before and after administration of DKT. Si...

Background. Congenital malformations of the gastrointestinal (GI) tract are common birth defects detected in neonatal period and usually present with signs GI obstruction which at times can be life threatening. Anorectal among more frequent congenital anomalies. The co-occurrence heart defect (CHD) along malformation significantly affect natural history either defect. Purpose - to study prevale...

BACKGROUND/PURPOSE Most surgeons recommend daily dilatation after surgery for Hirschsprung disease and anorectal malformations. Our goal was to critically evaluate the potential risks and benefits of this practice. METHODS A retrospective chart review was carried out of all children undergoing repair of Hirschsprung disease or anorectal malformation over 5 years. Patients with long segment Hi...