cavernous hemangioma is a rare benign tumor of the internal auditory canal (iac) of which fourteen cases have been reported so far. tinnitus and progressive sensorineural hearing loss (snhl) are the chief complaints of the patients. audiological and radiological planes, ctscan, and magnetic resonance image (mri) studies are helpful in diagnosis. the only choice of treatment is surgery with elec...

This studied examined vowel perception in young adults of normal hearing and hearing impaired with a mild to severe sensorineural hearing loss (SNHL) listeners. Stimuli were presented at conversational level and were recorded, digitized, and edited syllables. The stimuli were broken down into varying transitions. Listeners discriminated the audio presented selected corresponding stimuli option ...

UNLABELLED Auditory neuropathy spectrum disorder (ANSD) is characterized by impairment of the auditory nerve associated with preservation of outer hair cell function. OBJECTIVE To establish the prevalence of ANSD in subjects with sensorineural hearing loss (SNHL). METHOD This retrospective study was carried out between 2010 and 2012 and included the charts of 2,292 individuals with SNHL. Da...

Objectives: Hearing impairment in children is considered as an important public health problem. Auditory function in these children is poor and depends on their hearing aids efficacy and also their ears’ status. Hearing aids are very expensive and ear disease deteriorates its performance. Therefore detecting the ear disease and offering proper treatment is necessary. The aim of this study is to...

Diagnosing and treating hearing impairment is challenging because people with similar degrees of sensorineural hearing loss (SNHL) often have different speech-recognition abilities. The speech-based envelope power spectrum model (sEPSM) has demonstrated that the signal-to-noise ratio (SNRENV) from a modulation filter bank provides a robust speech-intelligibility measure across a wider range of ...

OBJECTIVE In an attempt to investigate the presence of hearing loss in primary Sjögren's syndrome (SS) patients and to determine the factors that might be involved in its pathogenesis, we prospectively evaluated 45 female SS patients with a mean age of 56.8 +/- 9.23 years and a mean disease duration of 8.32 +/- 5.39 years. METHODS Forty patients underwent a complete ear-nose-throat physical e...

CDH23 mutations have mostly been associated with prelingual severe-to-profound sensorineural hearing loss (SNHL) in either syndromic or nonsyndromic SNHL (DFNB12). Herein, we demonstrate the contribution of CDH23 mutations to postlingual nonsyndromic SNHL (NS-SNHL). We screened 32 Korean adult probands with postlingual NS-SNHL sporadically or in autosomal recessive fashion using targeted panel ...

CMV is a ubiquitous human herpesvirus that causes a lifelong, persistent infection in its host. Whereas primary CMV infections in otherwise healthy individuals are typically asymptomatic and go unnoticed, complications can develop in immunosuppressed individuals following acute CMV infection or CMV reactivation, presenting as retinitis, hepatitis, pneumonitis, gastroenteritis, or other end-orga...

Mutations of MYO15A are generally known to cause severe to profound hearing loss throughout all frequencies. Here, we found two novel MYO15A mutations, c.3871C>T (p.L1291F) and c.5835T>G (p.Y1945X) in an affected individual carrying congenital profound sensorineural hearing loss (SNHL) through targeted resequencing of 134 known deafness genes. The variant, p.L1291F and p.Y1945X, resided in the ...