introduction: the aim of this study was to evaluate the efficacy of combined intratympanic and systemic steroid therapy compared with systemic steroid therapy alone in idiopathic sudden sensorineural hearing loss (issnhl) patients with poor prognostic factors.     materials and methods: seventy-seven patients with sudden sensorineural hearing loss (ssnhl) who had at least one poor prognostic fa...

A novel approach to hearing-aid signal processing is described, which attempts to re-establish a normal neural representation in the sensorineural impaired auditory system. Most hearing-aid 5tting procedures are based on heuristics or some initial qualitative theory. These theories, such as loudness normalization, loudness equalization or maximal intelligibility can give vastly di(erent results...

Background. Sudden sensorineural hearing loss (SSHL) caused by opiate abuse or overuse has been well documented in the medical literature. Most documented case reports have involved either heroin or hydrocodone/acetaminophen. Recently, case reposts of methadone induced SSHL have been published. Case Report. We present the case of a 31-year-old man who developed SSHL after a methadone overdose i...

Acute sensorineural hearing loss may appear in some autoimmune diseases. Authors presented a case of 31 years old pregnant woman with Leśniowski-Crohn disease, in who acute total deafness of one ear and sensorineural hearing loss in the second ear appeared after she got pregnant. Immunological etiology was confirmed by presence of antinuclear and anti-type II collagen antibodies. Hearing level ...

BACKGROUND Congenital rubella syndrome (CRS) can be prevented with appropriate vaccination programs. The prevalence rates of rubella and CRS in Iran are unknown; therefore, the risk of exposure in pregnant women is not clear. The prevalence of CRS in the pre-vaccine period can be estimated by evaluating the proportion of children in the population with sensorineural hearing loss attributable to...

DFNA9 is a late-onset, progressive, autosomal dominantly inherited sensorineural hearing loss with vestibular dysfunction, which is caused by mutations in the COCH (coagulation factor C homology) gene. In this study, we investigated a Chinese family segregating autosomal dominant nonsyndromic sensorineural hearing loss. We identified a missense mutation c.T275A p.V92D in the LCCL domain of COCH...

UNLABELLED Increased life expectancy raises demands for special attention for the elderly population; speech, language and hearing science deals with their communication disorders. Hearing loss is a common disorder affecting this age group. It is known that the auditory feedback system is essential to human vocalizing, as it organizes voice production. AIM To assess and correlate the hearing ...

INTRODUCTION: Large vestibular aqueduct syndrome, or enlarged endolymphatic duct (EED) and sac (EFS) syndrome, is an inner ear malformation which manifests itself as progressive sensorineural hearing loss starting in infancy or childhood. The deformity of the endolymphatic duct and sac is congenital: however, the hearing loss that develops in this syndrome is acquired. A characteristic feature ...

Mitochondrial diseases (MD) are a clinically heterogeneous group of disorders that arise as a result of dysfunction of the mitochondrial respiratory chain. Sensorineural hearing loss (SNHL) is often associated to mitochondrial dysfunctions both in syndromic, nonsyndromic forms. SNHL has been described in association to different mitochondrial multisystemic syndromes, often characterized by an i...