نتایج جستجو برای: poikiloderma with neutropenia syndrome
تعداد نتایج: 9376087 فیلتر نتایج به سال:
Good's syndrome is a rare cause of immunodeficiency in adults associated with thymoma. We describe an 80-year-old female with chronic diarrhea, multiple opportunistic infections, and cytopenias. She underwent a thymectomy 5 years ago for a thymoma. Laboratory tests revealed neutropenia, hypogammaglobulinaemia, complete B-cell lymphopenia, and low CD4 T cells with inverted CD4:CD8 ratio, which i...
Locked-in syndrome is a rare clinical syndrome due to basilary artery thrombosis generally associated with trauma, vascular, or cardiac malformation. It can present as various types of clinical evolution and occasionally masquerades as other pathological conditions, such as infective meningoencephalitis. These complications are the cause of diagnostic delay, if not promptly recognised, followed...
BACKGROUND AND AIMS This was a safety and efficacy pharmacogenetic study of a previously performed randomized trial which compared the effectiveness of treatment of hepatitis C virus infection with pegylated interferon alpha (pegIFNα) 2a vs. 2b, both with ribavirin, for 48 weeks, in HCV-HIV coinfected patients. METHODS The study groups were made of 99 patients (efficacy pharmacogenetic substu...
T-cell Large Granular Lymphocytic Leukemia and Felty Syndrome in Rheumatoid Arthritis: A Case Report
T-cell large granular lymphocytic (LGL) leukemia is characterized by a clonal proliferation of CD3+ T-cells and has been associated with rheumatoid arthritis (RA). Splenomegaly common finding majority cases present cytopenia. Felty syndrome (FS) neutropenia splenomegaly also classically described in the literature for its association RA. Similarities clinical features, pathogenesis, management,...
Felty's syndrome, first reported by Felty in 1924 [1], is well known as a trio of rheumatoid arthritis, splenomegaly, and neutropenia, which occurs in 1-5% of patients with rheumatoid arthritis. The nephropathy associated with Felty's syndrome is very rare; we found only one previous case in the literature [2]. Although the pathogenesis of Felty's syndrome is still unclear, the glomerular lesio...
Felty's syndrome, first reported by Felty in 1924 [1], is well known as a trio of rheumatoid arthritis, splenomegaly, and neutropenia, which occurs in 1-5% of patients with rheumatoid arthritis. The nephropathy associated with Felty's syndrome is very rare; we found only one previous case in the literature [2]. Although the pathogenesis of Felty's syndrome is still unclear, the glomerular lesio...
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