نتایج جستجو برای: pms2

تعداد نتایج: 505  

Journal: :GE Portuguese journal of gastroenterology 2017
Sara Campos Pedro Amaro Inês Cunha João Fraga Maria Augusta Cipriano Luís Tomé

Introduction Lynch syndrome (LS), the most common hereditary colorectal cancer syndrome, is characterized by mutations in mismatch repair (MMR) genes leading to an increased cancer risk, namely colorectal cancer. Case In the context of surveillance colonoscopy, a 40-mm flat lesion (0-IIa+b, Paris classification) was identified and submitted to piecemeal mucosal endoscopic resection in a 64-ye...

2013
Medini Manohar Ghodgaonkar Federico Lazzaro Maite Olivera-Pimentel Mariela Artola-Borán Petr Cejka Martin A. Reijns Andrew P. Jackson Paolo Plevani Marco Muzi-Falconi Josef Jiricny

To improve replication fidelity, mismatch repair (MMR) must detect non-Watson-Crick base pairs and direct their repair to the nascent DNA strand. Eukaryotic MMR in vitro requires pre-existing strand discontinuities for initiation; consequently, it has been postulated that MMR in vivo initiates at Okazaki fragment termini in the lagging strand and at nicks generated in the leading strand by the ...

Journal: :Cell 1996
Winfried Edelmann Paula E Cohen Michael Kane Kirkland Lau Bernice Morrow Samuel Bennett Asad Umar Thomas Kunkel Giorgio Cattoretti Raju Chaganti Jeffrey W Pollard Richard D Kolodner Raju Kucherlapati

Germ line mutations in DNA mismatch repair genes including MLH1 cause hereditary nonpolyposis colon cancer. To understand the role of MLH1 in normal growth and development, we generated mice that have a null mutation of this gene. Mice homozygous for this mutation show a replication error phenotype, and extracts of these cells are deficient in mismatch repair activity. Homozygous mutant males s...

Journal: :Journal of medical genetics 2009
M P Hitchins R L Ward

Hereditary non-polyposis colorectal cancer (HNPCC) is an autosomal dominant syndrome characterised by a predisposition to early onset colorectal, endometrial and other cancers. The tumours typically exhibit microsatellite instability due to defective mismatch repair. HNPCC is classically caused by heterozygous loss-of-function mutations within the mismatch repair genes MLH1, MSH2, MSH6 and PMS2...

Journal: :Ceskoslovenska patologie 2017
Kristýna Němejcová Pavel Dundr Jana Rosmusová Inna Tučková

We report the case of a 44-year-old female with sebaceous adenoma arising in mature cystic teratoma of the ovary. The patient had a tumor in the left ovary; 125 x 90 x 70 mm. Microscopically, the tumor consisted of structures typical of dermoid cysts. However, large areas of sebaceous proliferation were found. These areas were comprised of sebaceous nodules with features similar to a sebaceous ...

Journal: :Pathologica 2016
A Remo M Fassan G Lanza

Microsatellite instability (MSI) is a hypermutable phenotype that usually arises from either a germline mutation in components of the mismatch repair (MMR) machinery (i.e. hMLH1, MSH2, MSH6 and PMS2) in patients with Lynch syndrome (LS) or somatic hypermethylation of the hMLH1 promoter in sporadic carcinomas. In all colorectal cancers (CRC) is possible to identify the MMR deficiency through pro...

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