how to cite this article: zamani gh.r. neuroimaging findings in storages disease of children. iran j child neurol. 2015 autumn;9:4(suppl.1): 10. pls see pdf.

patients with organic acidemia are prone to different infections, which lead to acidosis episodes. some studies have evaluated the status of immune system in acidotic phase in these patients, but to the best of our knowledge no study has evaluated the immune system in non-acidotic phase of the disease. in this study, thirty-one patients with organic acidemia were enrolled. for evaluation of hum...

in this case report we will describe a rare association between anhyrotic ectodermal dysplasia (aed) and immunodeficiency and autoimmunity [in our case: idiopathic thrombocytopenic purpura (itp) and crohn disease]. aed is a rare congenital disorder characterized by sparse hair, abnormal teeth and anhidrosis due to lack of eccrine glands. the survey of 87 cases with (aed) revealed only one irrit...

nelson’s syndrome nowadays a rare entity results from an adrenocorticotropin (acth)–secreting pituitary adenoma in patients with refractory cushing's disease after a therapeutic bilateral adrenal gland removal. we report a case of 25 year old female with cushing’s disease who was initially managed with medical treatment, but in view of severe persistent hyper cortisol state was subjected t...

background von hippel-lindau (vhl) disease is a hereditary, autosomal dominant syndrome which is manifested by a range of different benign and malignant tumors. this disease can present with different clinical presentations such as; retinal angioma (ra), hemangioblastoma (hb) of the central nervous system (cns), pheochromocytoma (pheo), and epididymal cystadenoma. tumors are usually accompanied...

background: hypertension is a significant public health concern of world‑wide distribution and is also the most common cardiovascular disease risk factor. adequate control of blood pressure is a critical element in the prevention of hypertension induced‑organ damage and life‑threatening complications. prevention of hypertension is possible and early detection and effective treatment can signifi...

background: expanding cities with rapid economic development has resulted in increased energy consumption leading to numerous environmental problems for their residents. the aim of this study was to investigate the correlation between air pollution and mortality rate due to cardiovascular and respiratory diseases in shiraz. methods: this is an analytical cross‑sectional study in which the corre...

background: hemodialysis patients are exposed to different stressful factors and have to use coping strategies as supportive processes. the goal of the present study is to investigate coping styles of hemodialysis patients. materials and methods: this is a descriptive analytical study conducted on 96 patients referring to hemodialysis centers affiliated to isfahan university of medical sciences...

background: spiritual well-being (swb) of patients with cardiovascular diseases particularly in those admitted in coronary care unit (ccu) is threatened due to disease crisis. therefore, implementing spiritual care is necessary for them. this study aimed to determine the effect of spiritual care program on swb of patients with cardiac ischemia admitted in ccu in al-zahra hospital, isfahan, iran...

three subheadings including treatment, prevention and control and diagnosis methods got the most priorities, respectively. although about half of the priorities are related to two subheadings including treatment and diagnosis methods, research priorities of prevention and control methods (22% of all priorities) indicate the importance of prevention for clinicians who gave scores to the titles. ...