نتایج جستجو برای: azf microdeletion

تعداد نتایج: 1732  

Journal: :JCI insight 2016
Hani Bagheri Chansonette Badduke Ying Qiao Rita Colnaghi Iga Abramowicz Diana Alcantara Christopher Dunham Jiadi Wen Robert S Wildin Malgorzata J M Nowaczyk Jennifer Eichmeyer Anna Lehman Bruno Maranda Sally Martell Xianghong Shan Suzanne M E Lewis Mark O'Driscoll Cheryl Y Gregory-Evans Evica Rajcan-Separovic

The 2p15p16.1 microdeletion syndrome has a core phenotype consisting of intellectual disability, microcephaly, hypotonia, delayed growth, common craniofacial features, and digital anomalies. So far, more than 20 cases of 2p15p16.1 microdeletion syndrome have been reported in the literature; however, the size of the deletions and their breakpoints vary, making it difficult to identify the candid...

Journal: :Biological psychiatry 2014
Kim Fejgin Jacob Nielsen Michelle R Birknow Jesper F Bastlund Vibeke Nielsen Jes B Lauridsen Hreinn Stefansson Stacy Steinberg Helge B D Sorensen Troels E Mortensen Peter H Larsen Ib V Klewe Søren V Rasmussen Kari Stefansson Thomas M Werge Pekka Kallunki Kenneth V Christensen Michael Didriksen

BACKGROUND Genome-wide scans have uncovered rare copy number variants conferring high risk of psychiatric disorders. The 15q13.3 microdeletion is associated with a considerably increased risk of idiopathic generalized epilepsy, intellectual disability, and schizophrenia. METHODS A 15q13.3 microdeletion mouse model (Df[h15q13]/+) was generated by hemizygous deletion of the orthologous region a...

Journal: :JOURNAL OF CLINICAL AND DIAGNOSTIC RESEARCH 2018

1997
John J. Enyeart Juan Carlos Gomora Lin Xu Judith A. Enyeart

Bovine adrenal zona fasciculata (AZF) cells express a noninactivating K 1 current (I AC ) that is inhibited by adrenocorticotropic hormone and angiotensin II at subnanomolar concentrations. Since I AC appears to set the membrane potential of AZF cells, these channels may function critically in coupling peptide receptors to membrane depolarization, Ca 2 1 entry, and cortisol secretion. I AC chan...

Journal: :Pediatrics 2001

This set of guidelines is designed to assist the pediatrician to care for children with Williams syndrome diagnosed by clinical features and with regional chromosomal microdeletion confirmed by fluorescence in situ hybridization.

Journal: :American Journal of Medical Genetics 2021

Three unrelated patients with similar microdeletions of chromosome 14q32.11 shared phenotypes including language and developmental delay, four overlapping genes -CALM1, TTC7B, PSMC1, RPS6KA5 have been presented. All are expressed in the brain haploinsufficiency scores, which reflect low tolerance to loss function variation. An insight on region, may influence resulting phenotype has provided. G...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2014
Shujia Zhu Morgane Riou C Andrea Yao Stéphanie Carvalho Pamela C Rodriguez Olivier Bensaude Pierre Paoletti Shixin Ye

Reprogramming receptors to artificially respond to light has strong potential for molecular studies and interrogation of biological functions. Here, we design a light-controlled ionotropic glutamate receptor by genetically encoding a photoreactive unnatural amino acid (UAA). The photo-cross-linker p-azido-L-phenylalanine (AzF) was encoded in NMDA receptors (NMDARs), a class of glutamate-gated i...

Journal: :Genetics and molecular research : GMR 2007
J T Arruda B M Bordin P R Santos W E J C Mesquita R C P C Silva M C S Maia M S Approbato R S Florêncio W N Amaral M A Rocha Filho K K V O Moura

Microdeletions in Yq are associated with defects in spermatogenesis, while those in the AZF region are considered critical for germ cell development. We examined microdeletions in the Y chromosomes of patients attended at the Laboratory of Human Reproduction of the Clinical Hospital of the Federal University of Goiás as part of a screening of patients who plan to undergo assisted reproduction. ...

Journal: :Journal of visualized experiments : JoVE 2013
Saranga Naganathan Amy Grunbeck He Tian Thomas Huber Thomas P Sakmar

To facilitate structural and dynamic studies of G protein-coupled receptor (GPCR) signaling complexes, new approaches are required to introduce informative probes or labels into expressed receptors that do not perturb receptor function. We used amber codon suppression technology to genetically-encode the unnatural amino acid, p-azido-L-phenylalanine (azF) at various targeted positions in GPCRs ...

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