نتایج جستجو برای: arylsulfatase b

تعداد نتایج: 899802  

Objective(s): Mucopolysaccharidosis VI (MPS VI) or Maroteaux-Lamy syndrome is a rare metabolic disorder, resulting from the deficient activity of the lysosomal enzyme arylsulfatase B (ARSB).  The enzymatic defect of ARSB leads to progressive lysosomal storage disorder and accumulation of glycosaminoglycan (GAG) dermatan sulfate (DS), which causes harmful effects on various organs and tissues an...

Journal: :The Journal of biological chemistry 2008
Elena Marie Wiegmann Eva Westendorf Ina Kalus Thomas H Pringle Torben Lübke Thomas Dierks

The human sulfatase family has 17 members, 13 of which have been characterized biochemically. These enzymes specifically hydrolyze sulfate esters in glycosaminoglycans, sulfolipids, or steroid sulfates, thereby playing key roles in cellular degradation, cell signaling, and hormone regulation. The loss of sulfatase activity has been linked to severe pathophysiological conditions such as lysosoma...

Journal: :Botanical Studies 2021

Abstract Background The soil quality and health of the tea plantations are dependent on agriculture management practices, long-term chemical fertilizer use is implicated in decline. Hence, several sustainable practices used to improve maintain quality. Here, this study, changes properties, enzymatic activity, dysbiosis bacterial community composition were compared using three agricultural namel...

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