Complex congenital heart defects (CHD) are associated with a variety of single gene abnormalities and chromosomal rearrangements. Of the various forms of CHD, aortic arch interruption, a conotruncal heart defect, is relatively uncommon. Here we report a male neonate with aortic arch interruption type B, secundum atrial septal defect, perimembranous ventricular septal defect, patent ductus arter...

Refer to the page 215-221 In this issue, Park et al. 1) present their experience with the use of a novel, fenestrated aortic arch stent graft (FASG) with a preloaded catheter for supra-aortic vessels. The authors have done an outstanding job highlighting a subject of increasing importance in acute clinical care, namely, performing thoracic endovascular aortic repair (TEVAR) in a short landing z...

We report a case of a young girl with Turner syndrome presenting with a pulsatile left-sided supraclavicular swelling since birth, which proved to be the rare anomaly of a cervical aortic arch. Though elongation of the transverse aortic arch is well known in Turner syndrome, to the best of our knowledge, a cervical aortic arch has not been described in the literature.

Although a newcomer to American medical literature, this strange vascular disease of young adult women has been recognized abroad for many years. The etiology is obscure, but the pathologic findings are fairly well documented and the clinical picture is unusually consistent. An obliterative arteritis of the branches of the aortic arch results in severe ocular and cerebral damage. The disease pr...

Takayasu arteritis (TA) is a chronic vasculitis that affects the aortic arch and its primary branches. Ulcerative colitis (UC) is an inflammatory bowel disease of unknown etiology. Patients diagnosed with both TA and UC have rarely been reported. The pathogenesis of TA and UC is uncertain, but cell-mediated mechanisms play an important role in both diseases, and a genetic factor is thought to h...

Right-sided aortic arch is a rare anomaly, and aortic dissection involving a right-sided aortic arch is extremely rare. We report the case of a 65-year-old man with a right-sided aortic arch and a right descending aortic dissection and a stent-graft was accurately deployed without perioperative complications. There were no any complaints and complications after 18 months follow-up. The CTA demo...

The surgical treatment of an aortic coarctation requires a resection of the stenotic area and direct suture of the aorta. An extended mobilization allows an enlargement of a hypoplastic distal aortic arch. In ductal dependent circulation, the distal aortic arch can be enlarged with a patch before tackling the coarctation itself. Postsurgical aortic arch stenoses often require a surgical interve...

An aberrant right subclavian artery described by David Bayford, is rare and one of the aortic arch anomalies. It gives usually incidental findings. We present case a 57-year-old woman who was admitted to neurology outpatient clinic due headache no obvious pathology detected during physical examination. In consequence brain chest CT angiography, anomalies branches were found asymptomatic bicarot...

Takayasu arteritis (also known as pulseless disease, aortoarteritis, and aortic arch syndrome) is a chronic, inflammatory and occlusive vasculitis of the aorta and its primary branches as well as the pulmonary arteries. It predominantly affects young females, particularly from India and South East Asia.Subclavian steal syndrome secondary to takayasu arteritis occurs when there is severe stenosi...

OBJECTIVES Hybrid endovascular procedures are rapidly evolving and have recently been adopted for high-risk patients deemed unsuitable for conventional aortic arch surgery. We describe here our initial experience with this technique, including the management of 2 patients who developed a retrograde type A aortic dissection post-de-branching. METHODS Between May 2010 and October 2012, 109 pati...