Unilateral Pulmonary Artery Agenesis (UPAA) is a rare congenital anomaly during the 4 th  week of gestational age. It is defined as an absence of pulmonary parenchyma and its supporting artery. A 9-year-old girl was admitted to our hospital because of chronic cough. Chest examination showed a decrement in lung sound of right hemi-thorax with expiratory wheeze. Chest radiography (CXR) revealed a...

Congenital pulmonary artery agenesis is a rare cardiovascular malformation, frequently oligosymptomatic,1,2 that can be complicated with unilateral pulmonary edema3 or pulmonary hypertension.1,2,4 We report the case of a patient with congenital pulmonary artery agenesis and pulmonary hypertension who developed unilateral pulmonary edema and discuss the role of sildenafil in pulmonary hypertensi...

Congenital pulmonary artery agenesis is a rare cardiovascular malformation, frequently oligosymptomatic,1,2 that can be complicated with unilateral pulmonary edema3 or pulmonary hypertension.1,2,4 We report the case of a patient with congenital pulmonary artery agenesis and pulmonary hypertension who developed unilateral pulmonary edema and discuss the role of sildenafil in pulmonary hypertensi...

unilateral pulmonary artery agenesis (upaa) is a rare congenital anomaly during the 4 th  week of gestational age. it is defined as an absence of pulmonary parenchyma and its supporting artery. a 9-year-old girl was admitted to our hospital because of chronic cough. chest examination showed a decrement in lung sound of right hemi-thorax with expiratory wheeze. chest radiography (cxr) revealed a...

BACKGROUND Fetal unilateral lung agenesis, complicated with cardiac shifting, is a rare anomaly, the diagnosis of which remains a challenge for many sonographers in routine screening programs. The present study describes a systematic approach for the diagnosis of fetal unilateral lung agenesis and cardiac malpositions in routine prenatal screening. METHODS A total of 18 cases of fetal unilate...

A 33-year-old woman with a history of psoriasis presented with asymmetric oligoarthritis. She had no cardiovascular symptoms. Naproxen and steroids were started with the diagnosis of psoriatic arthritis. Routine chest X-ray showed a small left hemithorax with a right-sided aortic arch and decreased left-sided pulmonary vasculature. A CTscan (Picture A) demonstrated the absence of the left pulmo...

INTRODUCTION Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. The clinical presentation is variable and many patients can be asymptomatic for many years and even throughout their lives. CASE PRESENTATION We report the case of a 53-year-old African-American woman who was diagnosed with righ...

Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. UAPA is usually associated with cardiac anomalies and surgically treated in childhood. We report a rare case of a 50-year-old woman who was diagnosed with left pulmonary artery agenesis without any other cardiac anomalies. Clinicians should be...

Unilateral pulmonary artery agenesis (UPAA) with pulmonary hypoplasia is a rare congenital anomaly. We describe a 71-year old male who was incidentally diagnosed with the right UPAA and a hypoplastic right lung supplied by collateralized right coronary.