Sjögren-Larsson syndrome is a rare autosomal recessive disorder that was originally recognized in the coexistence of congenital ichthyosis, spastic diplegia or quadriplegia and mental retardation. We recently saw two cases with characteristic features of this rare syndrome. Two brothers aged 21 and 25 years presented with triad of congenital ichthyosis, mental retardation and spastic diplegia. ...

[Purpose] The purpose of this study was to compare joint angles between normal children and those with spastic diplegia using three-dimensional gait analysis. [Subjects and Methods] The study subjects were eight patients with spastic diplegia and eight normal children. Three-dimensional gait analysis was used for the survey. The measured gait variables were the joints of the lower extremity in ...

This investigation quantified maximum active resultant joint torques in children with spastic diplegia cerebral palsy and nondisabled children. An isokinetic dynamometer rotated the limb (10°/s) while the resultant knee joint torques (both assistive and resistive) during knee extension and flexion in 6 nondisabled children and 26 children with cerebral palsy were recorded. Torque–angle data wer...

Introduction Ankle foot orthoses (AFOs) are prescribed for ambulatory children with spastic diplegia to improve biomechanical alignment and functional capability. Orthotic prescription is often based upon clinical experiences, treatment paradigms (biomechanical vs neurodevelopmental), and the perceived desires of the child/family. Previous investigations have reported that AFO use in ambulatory...

OBJECTIVE To investigate the co-ordination between reaching, ground reaction forces and muscle activity in standing children with severe spastic diplegia wearing dynamic ankle-foot orthoses compared with typically developing children. DESIGN Clinical experimental study. SUBJECTS Six children with spastic diplegia (Gross Motor Function Classification System level III-IV) and 6 controls. ME...

Botulinum toxin injections may significantly improve lower limb kinematics in gait of children with spastic forms of cerebral palsy. Here we aimed to analyze the effect of lower limb botulinum toxin injections on trunk postural control and lower limb intralimb (intersegmental) coordination in children with spastic diplegia or spastic hemiplegia (GMFCS I or II). We recorded tridimensional trunk ...

how to cite this article: dalvand h, dehghan l, feizi a, hosseini sa, amirsalari s. iran j child neurol. 2013 autumn; 7(4):12-19. abstract objective the purpose of this study was to examine the impacts of hinged and solid anklefoot orthoses (afos) on standing and walking abilities in children with spastic diplegia. materials & methods in a quasi-experimental design, 30 children with spastic dip...

Recent proposals of classification for cerebral palsy (CP), mainly revised for epidemiological purposes, suggest to abandon the use of the term diplegia. Conversely, in this paper data are presented to support the proposal to maintain the distinction between spastic tetraplegia and diplegia, and to subdivide this latter according to four main clinical patterns of walking observable in these chi...