نتایج جستجو برای: slc29a3 gene mutation

تعداد نتایج: 1284717  

2012
Alexandre Bolze Avinash Abhyankar Audrey V. Grant Bhavi Patel Ruchi Yadav Minji Byun Daniel Caillez Jean-Francois Emile Marçal Pastor-Anglada Laurent Abel Anne Puel Rajgopal Govindarajan Loic de Pontual Jean-Laurent Casanova

We investigated two siblings with granulomatous histiocytosis prominent in the nasal area, mimicking rhinoscleroma and Rosai-Dorfman syndrome. Genome-wide linkage analysis and whole-exome sequencing identified a homozygous frameshift deletion in SLC29A3, which encodes human equilibrative nucleoside transporter-3 (hENT3). Germline mutations in SLC29A3 have been reported in rare patients with a w...

Background: Mutation in NPM1 gene has been reported to be the most common genetic mutation in de novo acute myeloid leukemia (AML). AML with NPM1 gene mutation usually presents with higher initial leukocyte and blast cell counts and negative CD34 expression. We aimed to investigate the difference of initial leukocyte counts, bone marrow blast cell counts and expression of CD34 among patients wi...

Journal: :iranian journal of parasitology 0
soudabeh heidari parasitology and mycology dept. shahid beheshti university of medical sciences, tehran, iran. mojgan bandehpour cellular and molecular biology research center, shahid beheshti university of medical sciences, tehran, iran and biotechnology dept. shahid beheshti university of medical sciences, tehran, iran. seyyed-javad seyyed-tabaei parasitology and mycology dept. shahid beheshti university of medical sciences, tehran, iran. zarintaj valadkhani parasitology dept. pasteur institute of iran, tehran, iran. ali haghighi parasitology and mycology dept. shahid beheshti university of medical sciences, tehran, iran. alireza abadi social medicine dept. shahid beheshti university of medical sciences, tehran, iran.

background: trichomonas vaginalis causes trichomoniasis and metronidazole is its chosen drug for treatment. ferredoxin has role in electron transport and carbohydrate metabolism and the conversion of an inactive form of metronidazole (co) to its active form (cpr). ferredoxin gene mutations reduce gene expression and increase its resistance to metronidazole. in this study, the frequency of ferre...

2013
I Melki K Lambot L Jonard V Couloigner P Quartier B Neven B Bader-Meunier

Introduction Germline mutations in SLC29A3 result in a range of clinically related, recessive syndromes: H syndrome, pigmented hypertrichosis with insulin-dependent diabetes mellitus (PHID) syndrome, Faisalabad histiocytosis (FHC), and sinus histiocytosis with massive lymphadenopathy (SHML). Main symptoms of these diseases are hyperpigmentation with hypertrichosis, sensorineural deafness, diabe...

Journal: :iranian journal of blood and cancer 0
morteza karimipour sirous zeinali edward graham tuddenham nafiseh nafissi manijeh lak peter green

background: heterogeneous mutations in the human coagulation factor ix gene lead to an x-linked recessive bleeding disorder known as hemophilia b. the disease is distributed worldwide with no ethnic or geographical priority. materials and methods: the aim of this study was to characterize the factor ix gene mutations in 28 unrelated iranian hemophilia b patients. polymerase chain reaction (pcr)...

Journal: :iranian journal of allergy, asthma and immunology 0
zahra alizadeh immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, iran mohammad reza fazlollahi immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, iran massoud houshmand national institutes for genetics engineering and biotechnology, tehran, iran marzieh maddah immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, iran zahra chavoshzadeh pediatric infectious research center, mofid children hospital, shahid beheshti medical university, tehran, iran amir ali hamidieh hematology, oncology and stem cell transplantation research center, tehran university of medical sciences, tehran, iran

severe  congenital  neutropenia  (scn)  is  a  rare  primary  immunodeficiency   disease. different genes are found to be associated with scn, including ela2, hax1, was, gfi1, g-csfr  and  g6pc3.  the  aim  of  this  study  was  to  find  different  gene  mutations responsible for scn in iranian patients. twenty-seven   patients   with   scn  referred   to  immunology,   asthma   and  allergy r...

Journal: :international journal of advanced biological and biomedical research 2014
fatemeh amraei hedayatollah roshanfekr jamal fayazi mohammad bojarpour

objective: identity the genetic aspects and major gene influence on energy balance, milk production, fertility, food safety and consumer are the recent interests of genetic and breeding researchers. methods: najdi cattle is the most prominent breeds in khuzestan province. to do this plan in shoushtar najdi cattle station, blood samples were taken from 15 najdi cattles. dna was extracted from wh...

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