Rhabdomyosarcoma is a malignant mesenchymal soft tissue tumour with tendency towards skeletal muscle differentiation. It commonly seen in children and adolescents but exceedingly rare adults. The most common site adults the extremities. Less locations include pelvis thorax. diagnosed by morphologic presence of scattered pleomorphic rhabdomyoblasts immunohistochemistry (with evidence at least on...

BACKGROUND Malignant triton tumors are relatively rare and highly aggressive tumors in which malignant schwannoma cells coexist with rhabdomyoblasts. Their occurrence in the retroperitoneum is uncommon and has been rarely reported. CASE PRESENTATION We present the case of a patient with a retroperitoneal malignant triton tumor. A 32-year-old male was referred with epigastric pain and an abdom...

BACKGROUND Embryonal rhabdomyosarcoma in a form of a polyp of the uterine cervix occurs mainly in young women in their second decade of life. The characteristic microscopic features are: the submucosal cambium layer and the presence of rhabdomyoblasts in the stroma. So far the treatment has not been well defined and ranges from conservative to radical surgery CASE The presented case is a 22-y...

Rhabdomyosarcoma (RMS) represents a malignant tumor of skeletal muscle cells arising from rhabdomyoblasts. RMS represents the most common soft tissue sarcoma in children. In adults it is uncommon and accounts for less than 1% of all malignant solid tumors. While treatment protocols are well known for children, there is no standardized regimen in adults. This is one reason, why the outcome in ad...

Intraocular medulloepithelioma is a rare embryonal neoplasm that occurs predominantly in children and arises from the primitive medullary epithelium of the optic cup. Medulloepitheliomas that contain heterotopic elements or tissues such as brain, cartilage, or rhabdomyoblasts are classified as teratoid, and tumors lacking these elements are classified as nonteratoid medulloepitheliomas. Both no...

Sarcomas represent large and diverse group of malignant tumours, originating from mesenchymal cells. Nearly 15% of all childhood tumours and about 1% of all tumours in adults are sarcomas [1]. The incidence of adult soft tissue sarcomas in Europe is 5/100,000 [2]. Rhabdomyosarcoma accounts for 4.6% of all soft tissue sarcomas and it is the most common paediatric sarcoma, while it is extremely r...

A 55-year-old postmenopausal female presented with genital bleeding and lower abdominal mass. An abdominal MRI revealed a heterogeneously enhanced, 15 × 10 cm mass, completely filling the lumen of the enlarged uterus. The cytologic analysis of the mass showed tumor cells in small clusters and as individual cells showing hyperchromatic round to oval nuclei, and pleomorphic and occasionally unipo...

Malignant triton tumor (MTT) is a malignant peripheral nerve sheath tumor (MPNST) with rhabdomyoblastic differentiation. It is very rare and has an aggressive clinical course and poor prognosis. A 27-year-old male patient presented with complaints of difficulty in urination for 3 months. Computerized tomography (CT) imaging demonstrated a huge irregular mass localized in the prostate, with inva...

Background: malignant triton tumor is a very rare malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. In the present paper, we report aprimary malignant triton tumor in the heart of a 34-year-old woman who underwent resection of the left atrial tumor. To the best of our knowledge, this is the second case of primary malignant triton tumor of the heart repor...