Septate uterus is the most common structural anomaly of all mullerian defects. It is included in Class V of the AFS classification of anomalies of mullerian ducts. Fusion of the median septum of the mullerian ducts proceeds cephalad from the mullerian tubercle up to the junction of future round ligaments; shortly thereafter, the septum between the ducts is resorbed. Congenital defects can occur...

Unicornuate uterus is a rare congenital anomaly which occurs due to partial development of mullerian duct system. Patient with unicornuate uterus usually present with dysmenorrhoea, hematometra and endometriosis during their reproductive period. In the absence of these symptoms, proper identification and diagnosis of mullerian anomaly becomes difficult. Sometimes during laparoscopy it can mimic...

Obstructive mullerian anomalies give rise to a spectrum of clinical presentations and are uncommon in routine gynecologic practice. The patient usually becomes symptomatic in early reproductive years. Recurrent pelvic pain, dysmenorrhea, enlarging abdominopelvic mass, and abnormal vaginal discharge are the common presenting symptoms. We describe a rare case of a mullerian anomaly getting diagno...

Mayer Rokitansky Kuster Houser syndrome (MRKH syndrome) is characterized by Mullerian duct structures agenesis, vaginal atresia being the commonest variant. It can be associated with renal, skeletal, spine and other malformations. Patient with Mayer Rokitansky syndrome has a varied presentation from newborn period to adolescence. Thorough investigations are required for classification of the sy...

Herlyn werner wunderlich syndrome (HWWS) is a rare congenital mullerian ductal Anomaly (MDA) characterised by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. It generally occurs at puberty and exhibhits non-specific and variable symptoms with acute or chronic pelvic pain shortly following menarche, causing a delay in diagnosis. Moreover, the diagnosis is com...

Juvenile cystic adenomyoma is a rare form of adenomyosis and described as a new type of mullerian anomaly in literature. We are presenting two cases of juvenile cystic adenomyoma which were misdiagnosed preoperatively as unicornuate uterus with haematometra in a non-communicating rudimentary horn. The mainstay of treatment is complete resection of lesion.