نتایج جستجو برای: men2a

تعداد نتایج: 147  

Journal: :Cancer research 2000
K Kawai T Iwashita H Murakami N Hiraiwa A Yoshiki M Kusakabe K Ono K Iida A Nakayama M Takahashi

Germ line mutations of the RET proto-oncogene are responsible for the development of multiple endocrine neoplasia type 2A (MEN 2A), an inherited cancer syndrome characterized by medullary thyroid carcinoma, pheochromocytoma, and parathyroid hyperplasia. To study the mechanism of tissue-specific tumor development by RET with a MEN2A (cysteine 634-->arginine) mutation, we generated transgenic mic...

Journal: :The Journal of biological chemistry 2005
Barbara Frêche Patricia Guillaumot Julie Charmetant Ludivine Pelletier Celine Luquain Dale Christiansen Marc Billaud Serge N Manié

Dominant-activating mutations in the RET (rearranged during transfection) proto-oncogene, a receptor tyrosine kinase, are causally associated with the development of multiple endocrine neoplasia type 2A (MEN2A) syndrome. Such oncogenic RET mutations induce its ligand-independent constitutive activation, but whether it spreads identical signaling to ligand-induced signaling is uncertain. To addr...

Journal: :The Medical journal of Australia 1985
I R Gough

An adult woman 43 years old, with Multiple Endocrine Neoplasia type 2A (MEN2A). Clinical diagnosis of MEN2A was made based on the chief complaints of abdominal pain and a lump in the front left side area of neck accompanied with weight loss, from laboratory examination revealed an increased level of plasma levels of calcitonin levels with the result of 6359 pg/ml and 24 hours metanephrine urine...

Journal: :The Journal of the Association of Physicians of India 2012
Sudhi Agarwal Amit Agarwal Gyan Chand Sushil Kumar Gupta Manoj Jain Pooja Ramakant

Multiple endocrine neoplasia 2a (MEN2a) syndrome is one of the rare genetic disorder where prophylactic thyroidectomy is recommended for RET mutation carriers due to increased risk for developing MTC during lifetime. We present a case report of prophylactic total thyroidectomy in a family based on genetic screening that proved to be MTC on histopathology. This is the first reported case in Indi...

2013
Qin Cui Wen Wang Zhenzhen Fu Xin Shao Zhihong Zhang Mei Zhang Xianxia Ju Kunlin Wang Jiawei Chen Hongwen Zhou

Multiple endocrine neoplasia type 2A (MEN2A), a subtype of MEN2, is characterized by medullary thyroid cancer, pheochromocytoma, and primary hyperparathyroidism. A Han Chinese pedigree with MEN2A was investigated following confirmation of the proband's diagnosis by pathological findings and DNA/biochemical screening. DNA samples from 4 other family members were collected and exon 5, 8, 10, 11, ...

2017
Qiuli Liu Dali Tong Wenqiang Yuan Gaolei Liu Gang Yuan Weihua Lan Dianzheng Zhang Jun Zhang Zaoming Huang Yao Zhang Jun Jiang

BACKGROUD Multiple endocrine neoplasia type 2A (MEN2A) is a condition with inherited autosomal dominant mutations in RET (rearranged during transfection) gene that predisposes the carrier to extremely high risk of medullary thyroid cancer (MTC) and other MEN2A-associated tumors such as parathyroid cancer and/or pheochromocytoma. Little is reported about MEN2A syndrome in the Chinese population....

2013
Bas A Twigt Anouk Scholten Gerlof D Valk Inne HM Borel Rinkes Menno R Vriens

BACKGROUND Primary hyperparathyroidism (PHPT) is most commonly sporadic (sPHPT). However, sometimes PHPT develops as part of multiple endocrine neoplasia (MEN) type 1 or 2A. In all, parathyroidectomy is the only curative treatment. Nevertheless, there are important differences in clinical expression and treatment. METHODS We analyzed a consecutive cohort of patients treated for sporadic, MEN1...

Journal: :Clinical cancer research : an official journal of the American Association for Cancer Research 2002
Il-Jin Kim Hio Chung Kang Jae-Hyun Park Ja-Lok Ku Jong-Soo Lee Hyuk-Joon Kwon Kyong-Ah Yoon Seung Chul Heo Hee-Young Yang Bo Youn Cho Seong Yeon Kim Seung Keun Oh Yeo-Kyu Youn Do-Jun Park Myung-Shik Lee Kwang-Woo Lee Jae-Gahb Park

Multiple endocrine neoplasia type 2 (MEN2) syndromes are inherited in an autosomal dominant fashion with high penetrance. There are three subtypes, namely, MEN2A (multiple endocrine neoplasia type 2A), MEN2B (multiple endocrine neoplasia type 2B), and familial medullary thyroid carcinoma. The variations in the RET gene play an important role in the MEN2 syndromes. In this work, we have develope...

Journal: :Oncology nursing forum 2006
Ellen Giarelli

PURPOSE/OBJECTIVES To describe the kinds of self-monitoring activities and the emotional responses associated with those activities in patients with a genetic predisposition to multiple endocrine neoplasia type 2a (MEN2a) or familial adenomatous polyposis (FAP). RESEARCH APPROACH Thematic analysis of the transcripts of patient interviews conducted for two previous grounded theory investigatio...

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