Sudden death is a known but unpredictable complication of hypertrophic cardiomyopathy. We describe two patients who both had a strong family history of the disorder complicated by sudden death. Necropsy disclosed accessory bypass tracts, concealed in one and previously suspected in the other. One died from ventricular fibrillation and the other, who died outside hospital, had previously complai...

INTRODUCTION Background: The actual prognosis of hypertrophic cardiomyopathy, a disorder previously thought of to be notorious for an increased risk of untimely death is poorly defined. Objective: The present study describes the findings of patients with Hypertrophic Cardiomyopathy followed for more than nineteen years in a large clinic population. Materials and Methods: A clinic population of ...

BACKGROUND For more than 20 years in Italy, young athletes have been screened before participating in competitive sports. We assessed whether this strategy results in the prevention of sudden death from hypertrophic cardiomyopathy, a common cardiovascular cause of death in young athletes. METHODS We prospectively studied sudden deaths among athletes and nonathletes (35 years of age or less) i...

A case of cardiac arrest in a ten year old child that was successfully resuscitated is here presented. The etiological investigation showed an Hypertrophic Cardiomyopathy (HCM). An Implantable Cardioverter Defibrillator (ICD) was placed for secondary profilaxy of Sudden Death (SD). Sudden Death in paediatric age is a rare accident with bad prognosis (survival with no sequel inferior to 5%) and ...

We describe an uncommon association between Leopard syndrome and hypertrophic cardiomyopathy in a 27-year-old woman, who was little symptomatic and came for sudden death risk stratification and prevention. She has a rare syndrome, whose symptoms are maculae over the body and abnormalities in eyes, genital organs, heart and in growth. Association of hypertrophic cardiomyopathy with sudden death ...

T he incidence of sudden death in hypertrophic cardiomyopathy is 2-4% a year in adults and 4-6% a year in children and adolescents.1 These data have been generated from referral cardiac centers and may reflect a bias to the more severe patients.2 The identification and management of patients with hypertrophic cardiomyopathy who are at increased risk of sudden death remains a major problem, part...