نتایج جستجو برای: hyper ige syndrome

تعداد نتایج: 654501  

Journal: :International journal of pediatric otorhinolaryngology 2008
Krishnamurti Matos de Araujo Sarmento Shiro Tomita João Daniel Caliman e Gurgel

Dubowitz syndrome is a rare, autosomal recessive disorder characterized by intrauterine growth retardation, short stature, microcephaly, distinct facial dysmorphism, and psychomotoric retardation. The hyper-immunoglobulin E (hyper-IgE or Job syndrome) is a primary immunodeficiency characterized by recurrent staphylococcal abscesses, recurrent cyst-forming pneumonia, and an elevated serum IgE le...

2014
Chad J. Cooper Sarmad Said German T. Hernandez

Background. Hyper IgE is a rare systemic disease characterized by the clinical triad of high serum levels of IgE (>2000 IU/mL), eczema, and recurrent staphylococcal skin and lung infections. The presentation of hyper IgE syndrome is highly variable, which makes it easy to confuse the diagnosis with that of severe atopy or other rare immunodeficiency disorders. Case Report. A 23-year-old Hispani...

Journal: :Indian Journal of Dermatology 2018

2012
Suresh Kumar Angurana Renu Suthar Angurana

Journal: :Pakistan postgraduate medical institute 2023

Hyper-immunoglobulin E (IgE) is a disorder of immune system characterized by assemblage symptoms including recurrent skin and pulmonary infections, skeletal anomalies elevated serum IgE (>2000 IU/ml). More recently, apart from the typical features, neurological manifestations have also been described central nervous facial nerve palsy demyelinating disorders. Here we describe three patients ...

Journal: :Urology 2013
Pérsio Roxo Ullissis P Menezes Silvio Tucci Murilo F Andrade Gyl E Barros Silva Janaina Michelle Lima Melo

Kidney disease due to Aspergillus fumigatus is a rare finding in hyper-IgE syndrome. We report a patient with autosomal dominant hyper-IgE syndrome, recurrent pneumonia, and acute necrosuppurative pyelonephritis caused by Aspergillus fumigatus with a fatal outcome. We emphasize the severity and the difficulties in the management of renal complications that could be limiting the survival of thes...

ژورنال: :مجله دانشگاه علوم پزشکی مازندران 0
جواد بالاغفاری j ghafari faculty of medicine-mazandaran university of medical sciences, sari, iranفوق تخصص آلرژی ،آسم و ایمونولوژی اطفال، عضو هیأت علمی (استادیار) دانشگاه علوم پزشکی مازندران محمد قره گزلو m ghareh gozlou زینب نظری z nazari

سندرم ازدیاد hyper-ige syndrome) ige) یا job`s syndrom یک نقص ایمنی اولیه نادر با عفونت های مکرر مخصوصا عفونت های استافیلوککی، چهره خشن، ناهنجاری های اسکلتی و افزایش قابل ملاحظه سطح سرمی ige (بالای 2000iu/ml ) می باشد. بیمارآقای 16 ساله ای می باشد که به علت سرفه، تنگی نفس، اگزما و پنوماتوسل با سابقه عفونت های پوستی از 1 ماهگی مراجعه کرده و در بررسی های انجام شده سطح ige سرم بالا بوده که با تشخی...

Mansouri, Mahboubeh, Mesdaghi, Mehrnaz, Alimohammadi, Reza , Amirmoini, Mehrdad , Babaie, Delara , Chavoshzadeh, Zahra , Farajifard, Hamid , Mohammadzadeh, Iraj , Rahimi, Arezou , Rezaei, Nima ,

Background and Aims: Patients with Hyper-IgE syndrome suffer from fungal and bacterial infections, especially Candida albicans and Staphylococcus aureus. Due to the important role of T helper17 (Th17) lymphocytes in defense against fungal infections, the percentage of Th17 lymphocytes was studied in the patients with autosomal recessive hyper-IgE syndrome (AR-HIES). Materials and Methods: In...

Journal: :Journal of Nepal Paediatric Society 2015

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