Hemihypertrophy syndrome and cor triatriatum are extremely rare pathologies. Hemihypertrophy is defined as complete or partial overgrowth of one of the hemibodies. Cor triatriatum is a congenital heart disease characterized by a membrane which separates the left atrium into two chambers; if that membrane has a restrictive hole, it causes obstruction to blood passage from the pulmonary veins int...

Hemihypertrophy, or hemihyperplasia, is a condition in which there may be asymmetrical overgrowth of the cranium, face, trunk, and/or limbs on one side of the body. There may also be asymmetrical visceromegaly on the ipsilateral or contralateral side. Hemihypertrophy may occur in isolation, hence the term “isolated hemihypertrophy (IH)”, or as part of a number of overgrowth syndromes in which o...

Although the ancient Greek and Roman sculptors recognized that the human frame was not symmetrical, it was not until 1822 that Meckel pointed out variations in size and shape of the two halves of the body, and the first clinical report of a patient with hemihypertrophy was made by Wagner in 1839. Since that day there have been only just over 100 cases reported throughout the world claiming tota...

options and outcomes. J Hand Surg Eur Vol 2013;38:297-303. 3. Hoyme HE, Seaver LH, Jones KL, et al. Isolated hemihyperplasia (hemihypertrophy): report of a prospective multicenter study of the incidence of neoplasia and review. Am J Med Genet 1998;79:274-8. 4. Oren NC, Vurucu S, Karaman B, et al. Renal agenesis in a child with ipsilateral hemihypertrophy. Pediatr Nephrol 2010;25:1751-4. 5. West...

hepatoblastoma (hb) is a rare tumor of infancy and childhood manifesting with hepatomegaly and abdominal distention. it is seen with increased frequency in association with congenital hemihypertrophy and renal anomalies. metastases to other organs, including the lungs, lymph nodes and even ovaries is well known. but cerebral metastasis of this tumor, especially in the absence of metastasis to o...