Desmoplastic small round-cell tumor (DSRCT) is a rare and highly aggressive neoplasm of children and young adults that primarily arises from the abdomen with widespread peritoneal involvement and is characterized by distinct clinicopathologic features. Therapeuticmanagement of DSRCT remains challenging, and no standard therapy is currently described in the literature. Despite the combination of...

BACKGROUND The desmoplastic small round cell tumour is a rare and aggressive intra-abdominal neoplasia, with only 200 cases reported, and a higher incidence in men and predilection for the second decade of life. Histologically characterized by the presence of small nests of undifferentiated tumour cells, wrapped in fibrous desmoplastic stroma. CLINICAL CASE A 24 year old male started with abd...

7. Gerald WL, Ladanyi M, de Álava E at al. Clinical, Pathologic and molecular spectrum of tumors associated with t(11;22)(p13;q12): Desmoplastic small round cell tumorand its variants.J Olin Oncol 1998; 16: 3028-3036. 8. Antoneacu CR, Gerald WL, Magid MS at al. Molecular variants of the EWSWT1 gene fusion in desmoplastic small round cell tumor. Diagn Mol Pathol 1998; 7: 24-28. 9. de Álava E, La...

Desmoplastic small round cell tumor (DSRCT) is an extremely uncommon, highly aggressive, and malignant mesenchymal neoplasm of undetermined histogenesis. Less than 200 case reports have been documented in literature so far. Herein, we report a 26-year-old otherwise healthy female patient who presented with a 1-month history of epigastric pain. On physical examination, a palpable, slightly mobil...