Dermatofibrosarcoma protuberans (DFSP) is very rare tumor of dermis layer of skin with the incidence of only 1 case per million per year. DFSP rarely leads to a metastasis (Less than 5% have metastasis), but DFSP can recur locally. We publish a rare case of a recurrent dermatofibrosarcoma protuberans and its management with radical excision and interval skin grafting.

dermatofibrosarcoma protuberans is an uncommon malignant mesenchymal tumor of the dermis, which most commonly appears on the body and extremities. a preoperative diagnosis of dermatofibrosarcoma protuberans is extremely difficult, because it is a very rare entity and its appearance is often similar to that of benign breast lesion. here, we presented a case of breast dermatofibrosarcoma protuber...

Dermatofibrosarcoma protuberans is a relatively uncommon soft tissue tumor involving the dermal layer of skin with intermediate-to-low grade malignancy. Although metastasis rarely occurs, Dermatofibrosarcoma protuberans is a locally aggressive tumor with a high recurrence rate. We treated a 35-year-old male patient with Dermatofibrosarcoma protuberans left breast at Pakistan Air Force hospital ...

INTRODUCTION Dermatofibrosarcoma protuberans is a rare low-grade soft tissue neoplasm with trunk and extremities being the most common sites of involvement. We report a rare case of male breast with dermatofibrosarcoma protuberans and its imaging features. To our knowledge the imaging appearance of dermatofibrosarcoma protuberans of the breast has never been reported in the literature. CASE P...

INTRODUCTION Dermatofibrosarcoma protuberans is a rare, locally aggressive cutaneous tumor of intermediate to low-grade malignancy. COL1A1-PDGFβ translocation is specific to dermatofibrosarcoma protuberans, where the abnormally fused COL1A1-PDGFβ gene directs formation of an abnormal combined (fusion) protein that researchers believe to ultimately function like the platelet-derived growth facto...

dermatofibrosarcoma protruberans is a relatively uncommon slow growing, locally aggressive fibrous tumor of the skin. it has a prospensity of progressing to fibrosarcomatous change in 5% of the cases. we present a case of a 56 yr old male with presented to the outpatient department of surgery, sri siddhartha medical college, tumkur with a chest swelling in 2013. fnac was inconclusive and the ma...

Dermatofibrosarcoma protuberans (DFSP) is very rare tumor of dermis layer of skin with the incidence of only 1 case per million per year. DFSP rarely leads to a metastasis (Less than 5% have metastasis), but DFSP can recur locally. We publish a rare case of a recurrent dermatofibrosarcoma protuberans and its management with radical excision and interval skin grafting. 

Please cite this article as: el Hammoumi MM, Abouchadi A, Kabiri EH. Dermatofibrosarcoma gigante de la pared torácica anterior. Arch Bronconeumol. 2015;51:299-300. ∗ Corresponding author. E-mail address: [email protected] (M.M. el Hammoumi). dermatofibrosarcoma protuberans located in the skin above the sternon of a 31-year-old woman (Fig. 1) that was resected after pathological diagnosi...

Dermatofibrosarcoma protuberans (DFSP) has been described as a rare, locally invasive, malignant fibroblastic tumor with a high rate of recurrence that usually affects middle-aged patients. Herein, we describe a rare case of a pedunculated dermatofibrosarcoma protuberans of the right thumb in an 80-year-old woman treated with excision through the base of the pedicle. We also make a brief litera...

Curative surgical treatment of recurrent, locally advanced dermatofibrosarcoma protuberans is often limited owing to a close relation of the tumor with important anatomical structures. Targeted therapy with imatinib, a tyrosine kinase inhibitor, may cause significant reduction of tumor volume, thereby enabling radical surgery. This treatment strategy, therefore, offers a chance of cure for sele...