We report on a 12 year old mentally retarded boy who presented at birth with bilateral knee dislocations, dislocation of the right hip, and general joint laxity. Cytogenetic studies showed a 49,XXXXY karyotype. Hyperlaxity of joints is known to occur in 49,XXXXY patients, but congenital knee dislocation has not been reported. Rarely in 49,XXXXY and 49,XXXXX syndromes Larsen-like features may be...

We have operated total knee arthroplasty in a patient with bilateral congenital dislocation of the patella treated with a different method in each knee.

Congenital permanent dislocation of the patella is a rare disorder of the knee joint in which the patella is permanently displaced, even in extension and is fixed on the lateral aspect of the femoral condyle. The dislocation is irreducible without surgical techniques. This rare condition is usually detected within the first decade of life, because of inability of active extension in the knee an...

Congenital lateral dislocation of the patella is a rare condition caused by displacement of the extensor mechanism of the knee, which occurs before or shortly after birth (Malkin 1932). The patella is small and cannot be replaced in its normal position except by operation. This type of dislocation differs from recurrent or habitual dislocation of the patella, which occurs during childhood or ad...

introduction arthrogryposis multiplex congenita (amc) with incidence of 1 in 3000 of births is characterized by multiple rigid joint and soft-tissue contractures. case presentation we present a case of amc with severe soft tissue and joints contractures, especially joints of lower limb and elbows, bilateral complete dislocation of hips (cdh) and knees (cdk) (type iii), bilateral elbow joint dis...

Congenital patellar dislocation is a rare condition in which the patella is permanently dislocated and cannot be reduced manually. The patella develops normally as a sesamoid bone of the femur. This congenital dislocation results from failure of the internal rotation of the myotome that forms the femur, quadriceps muscle and extensor apparatus. It usually manifests immediately after birth, alth...