REFERENCES 1. Teo C, Nakaji P, Serisier D, et al. Resolution of trigeminal neuralgia following third ventriculostomy for hydrocephalus associated with Chiari I malformation: case report. Minim Invasive Neurosurg 2005;48:302e5. 2. Caranci G, Mercurio A, Altieri M, et al. Trigeminal neuralgia as the sole manifestation of an Arnold-Chiari type I malformation: case report. Headache 2008;48:625e7. 3...

Cerebral computed tomography (CT) is the primary imaging modality in the investigation of suspected cerebellar degeneration. A case is presented in which an inaccurate clinical and radiologic diagnosis of olivo-pontocerebellar degeneration resulted from CT imaging demonstrating loss of cerebellar substance. Subsequent clinical recognition of downbeat nystagmus led to a diagnosis of Chiari malfo...

We report a child with osteopetrosis, oxycephaly and Chiari type I malformation who presented with raised intracranial pressure. During cranial expansion surgery the patient developed sudden cardiac arrest which we believe was probably related to the Chiari malformation. The case highlights a previously unrecognized association between osteopetrosis, craniosynostosis and a persistently open fon...

Herniation of the hindbrain outside of the setting of intracranial hypertension, trauma, and brain tumors is an uncommon phenomenon with estimated incidence of less than 1%. In the late 1890's, Hans Chiari, a German pathologist, classified hindbrain herniation into three forms. This classification was then extended to include six types. We reviewed the current literature for the proposed embryo...

Chiari malformation is a congenital anomaly that primarily involves the downward displacement of the cerebellar tonsils through the foramen magnum and elongation of forth ventricle and lower brainstem. Patients with Chiari I (congenital or acquired) malformation are asymptomatic or may present with neurologic signs and symptoms. It is always a question of safety of neuraxial anesthesia in these...

This article reports the largest familial aggregation of Chiari malformation in a single family to date as reported in the literature. This study is a retrospective case series of a family of whom five individuals have a confirmed case of Chiari malformation and three additional individuals have Chiari signs and symptoms. This contribution further supports the implication of genetics in the tra...

Chiari malformation type III is an extremely rare anomaly characterized by a small posterior fossa and a low occipital/high cervical encephalocele with herniation of the posterior fossa contents (that is, the cerebellum and/or the brainstem, occipital lobe, and fourth ventricle). We report a case of Chiari malformation type III in a neonate, discuss the etiopathogenetic and radiological feature...

Recently, Iskandar et al described "Chiari Zero malformation" to characterize some kind of syringomyelia that exhibits classic Chiari-type symptoms with little to no herniation, but there is some dilemma about whether it is actually present. We presented a 38-year-old-man with a diagnosis of cervical syringomyelia. In his neurological examination, there was monoparesia at the left leg together ...

The authors describe a rare case of Chiari type I malformation presenting as persistent dysphagia. A fifty-eight year-old woman showing a nearly one-year history of swallowing difficulty was transferred to our department for neurological evaluation of aspiration pneumonia. Neurological examination revealed absence of bilateral gag reflexes, and mild weakness of the right upper extremity. Magnet...

A small percentage of individuals have the neurological anomaly of central precocious puberty (CPP). Common neurologic causes of CPP include a tumor or congenital lesions. Although Arnold-Chiari malformation can be caused by congenital or acquired causes, it is unusual in patients with CPP. We present the case of a girl aged 4.5 years who complained of breast budding. Her neurological examinati...