BACKGROUND Sturge-Weber syndrome is a rare congenital neuro- oculo- cutaneous disorder. OBJECTIVE To report a very rare unusual case of bilateral manifestation of Sturge Weber syndrome. CASE We report an unusual case of a 17-year-old female with advanced stage of bilateral glaucoma associated with facial nevus extending to the other half of the face as well and bilateral intracranial calcif...

Oculodermal melanocytosis, also known as Nevus of Ota, is a hamartomatous melanocytic nevus of dermal melanocytes. It presents as a bluish grey patch on the face, which may be congenital or acquired involving the area of distribution of the ophthalmic and maxillary branches of the trigeminal nerve. The nevus can be unilateral or bilateral, and, in addition to skin, it may involve ocular and ora...

Both acquired bilateral nevus of Ota-like macules (ABNOM) and nevus of Ota are characterized by the presence of dermal melanocytes. There are no differences in the method of treatment, however, postinflammatory hyperpigmentation (PIH) develops more often in ABNOM than in nevus of Ota following treatment. We investigated the differences in the development of PIH after treatment between ABNOM and...

The dentigerous cyst is one of the most common developmental odontogenic cysts in the jaw. Occurrence of the bilateral dentigerous cyst is uncommon, and frequently associated with syndromes like basal cell nevus syndrome or cleidocranial dysplasia. There are few reports on the presence of bilateral dentigerous cyst in nonsyndromic patients, and most of these are associated with first and third ...

Actas Dermosifiliogr. 2009;100:615-34 626 some forms of brain tumor; although such outcomes have not been demonstrated for melanoma. The cells of retinoblastoma, melanoma and dysplastic nevus are derived from the neural crest. There are authors who postulate that patients with retinoblastoma and dysplastic nevus syndrome have increased genetic susceptibility to melanoma due to a primary anomaly...

Nevus of Ota is a rare congenital hamartoma the dermal melanocytes causing blue-grey hyperpigmentation eye and adnexa. The condition usually unilateral but rarely it can be bilateral. A 28-year-old lady from West Bengal, India, visited Ophthalmology outpatient department with complaints blackish discoloration left side face periorbital region. On examination, large (5x6 cm) lesion was noted on ...