نتایج جستجو برای: bcl11a

تعداد نتایج: 301  

Journal: :Molecular and cellular biology 2013
Baeck-seung Lee Joseph D Dekker Bum-kyu Lee Vishwanath R Iyer Barry P Sleckman Arthur L Shaffer Gregory C Ippolito Philip W Tucker

Recombination-activating gene 1 protein (RAG1) and RAG2 are critical enzymes for initiating variable-diversity-joining (VDJ) segment recombination, an essential process for antigen receptor expression and lymphocyte development. The transcription factor BCL11A is required for B cell development, but its molecular function(s) in B cell fate specification and commitment is unknown. We show here t...

2017
Chen-Han Zhang Jue Wang Lin-Xin Zhang Yi-Han Lu Tian-Hao Ji Lu Xu Li-Jun Ling

Tamoxifen resistance is a serious problem in the endocrine therapy of breast cancer. Long non-coding RNAs play important roles in tumor development. In this study, we revealed the involvement of lncRNA uc.57 and its downstream gene BCL11A in TAM resistance. Tamoxifen-resistant MCF-7R cells showed lower expression of uc.57 and higher expression of BCL11A mRNA and protein than the parental MCF-7 ...

2017
Jessica Gasparello Enrica Fabbri Nicoletta Bianchi Giulia Breveglieri Cristina Zuccato Monica Borgatti Roberto Gambari Alessia Finotti

The involvement of microRNAs in the control of repressors of human γ-globin gene transcription has been firmly demonstrated, as described for the miR-486-3p mediated down-regulation of BCL11A. On the other hand, we have reported that miR-210 is involved in erythroid differentiation and, possibly, in γ-globin gene up-regulation. In the present study, we have identified the coding sequence of BCL...

2012
Yong Yu Juexuan Wang Walid Khaled Shannon Burke Peng Li Xiongfeng Chen Wei Yang Nancy A. Jenkins Neal G. Copeland Shujun Zhang Pentao Liu

Transcription factors play important roles in lymphopoiesis. We have previously demonstrated that Bcl11a is essential for normal lymphocyte development in the mouse embryo. We report here that, in the adult mouse, Bcl11a is expressed in most hematopoietic cells and is highly enriched in B cells, early T cell progenitors, common lymphoid progenitors (CLPs), and hematopoietic stem cells (HSCs). I...

2017
Jian Zhou Yue Yang Duo Zhang Liang Zhou Lei Tao Li-Ming Lu

OBJECTIVE We investigated the association between B-cell lymphoma/leukaemia 11A (BCL11A) rs11886868 and rs4671393 polymorphism, plasma BCL11A concentration, and the hazard of developing laryngeal squamous cell carcinoma (LSCC). PARTICIPANTS AND METHOD In this research, 330 LSCC patients, 310 healthy controls, and 155 vocal leukoplakia patients were genotyped for the BCL11A (rs11886868 C/T and...

Journal: :Genes & development 2010
Jian Xu Vijay G Sankaran Min Ni Tobias F Menne Rishi V Puram Woojin Kim Stuart H Orkin

The developmental switch from human fetal (gamma) to adult (beta) hemoglobin represents a clinically important example of developmental gene regulation. The transcription factor BCL11A is a central mediator of gamma-globin silencing and hemoglobin switching. Here we determine chromatin occupancy of BCL11A at the human beta-globin locus and other genomic regions in vivo by high-resolution chroma...

Journal: :The Journal of clinical investigation 2016
Christian Brendel Swaroopa Guda Raffaele Renella Daniel E Bauer Matthew C Canver Young-Jo Kim Matthew M Heeney Denise Klatt Jonathan Fogel Michael D Milsom Stuart H Orkin Richard I Gregory David A Williams

Reducing expression of the fetal hemoglobin (HbF) repressor BCL11A leads to a simultaneous increase in γ-globin expression and reduction in β-globin expression. Thus, there is interest in targeting BCL11A as a treatment for β-hemoglobinopathies, including sickle cell disease (SCD) and β-thalassemia. Here, we found that using optimized shRNAs embedded within an miRNA (shRNAmiR) architecture to a...

Journal: :The Journal of clinical investigation 2015
Anindita Basak Miroslava Hancarova Jacob C Ulirsch Tugce B Balci Marie Trkova Michal Pelisek Marketa Vlckova Katerina Muzikova Jaroslav Cermak Jan Trka David A Dyment Stuart H Orkin Mark J Daly Zdenek Sedlacek Vijay G Sankaran

A transition from fetal hemoglobin (HbF) to adult hemoglobin (HbA) normally occurs within a few months after birth. Increased production of HbF after this period of infancy ameliorates clinical symptoms of the major disorders of adult β-hemoglobin: β-thalassemia and sickle cell disease. The transcription factor BCL11A silences HbF and has been an attractive therapeutic target for increasing HbF...

2017
Kai-Hsin Chang Sarah E. Smith Timothy Sullivan Kai Chen Qianhe Zhou Jason A. West Mei Liu Yingchun Liu Benjamin F. Vieira Chao Sun Vu P. Hong Mingxuan Zhang Xiao Yang Andreas Reik Fyodor D. Urnov Edward J. Rebar Michael C. Holmes Olivier Danos Haiyan Jiang Siyuan Tan

To develop an effective and sustainable cell therapy for sickle cell disease (SCD), we investigated the feasibility of targeted disruption of the BCL11A gene, either within exon 2 or at the GATAA motif in the intronic erythroid-specific enhancer, using zinc finger nucleases in human bone marrow (BM) CD34+ hematopoietic stem and progenitor cells (HSPCs). Both targeting strategies upregulated fet...

Journal: :Science 2008
Stephen Buratowski

then the causative SNP either has a non–tissue-specific effect on transcription, or it acts at the posttranscriptional level, an issue that remains to be resolved. Although the results are consistent with the long isoforms of BCL11A functioning to suppress HbF production in a dose-dependent manner, they do not distinguish between a direct effect on γ-globin gene expression and an indirect effec...

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