the purpose of this study is to investigate the age -related improvement of defecation function in high type anorectal malformation in relation to the assessment of the internal anal sphincter. the function of defecation was studied every 5 years up to 15 years postoperatively according to the japanese scoring system in our hospital in 50 patients operated for high type (recto-urethral fistula)...

Rectovestibular fistula is a rare variant of anorectal malformations. Such malformations are commonly operated in newborn period or puberty. So it is so uncommon to coincide with uncorrected rectovestibular fistula in women of reproductive ages. Herein, we report a case of multigravida pregnant woman with uncorrected rectovestibular fistula. The patient’s first pregnancy ended up by cesarean se...

Currarino syndrome is a rare congenital malformation characterised by the triad of: an anorectal malformation, sacral bony defect and presacral mass. One but possible anal canal duplication, anomaly which not only most distal also rarest form of digestive tract duplication. We present case four-year-old female who had complete including

This is a case report of 22-year-old girl admitted with abdominal distension, vomiting, and chronic constipation since birth. Abdomen was distended, and perineal examination revealed imperforate anus with vestibular fistula (ARM). So far worldwide very few cases have been reported about anorectal malformation presenting in adulthood, and thus extremely little data is available in the literature...

Anorectal Malformations are known to be associated with various other congenital anomalies including duodenal atresia. An association of congenital intrinsic duodenal obstruction causing partial duodenal obstruction in a patient with anorectal malformation is not described in literature. We describe a case of delayed presentation of congenital intrinsic duodenal obstruction in a child with high...

INTRODUCTION Anorectal malformation, one of the most common congenital defects, may present with a wide spectrum of defects. Almost all male patients present within first few days of life. CASE PRESENTATION A five-month-old baby boy of Indian origin and nationality presented with anal atresia and associated rectourethral prostatic fistula. The anatomy of the malformation and our patient's goo...

We report the case of a patient referred to our prenatal diagnostic unit due to the suspicion of spina bifida at 24 weeks gestation. Morphological assessment revealed rachischisis associated with Chiari type II, single kidney and anorectal malformation. The nonvisualization of the anal sphincter complex (ASC) on ultrasound led to the diagnosis of suspected high-type anorectal malformation (A,B ...

Congenital pouch colon is a condition of a shortened and pouch-like dilated colon and it is usually associated with an anorectal malformation. The pathogenesis and embryology of congenital pouch colon are not well understood, but dietary, environmental factors and familial inheritance may be contributing factors in this pathology. Most of the cases in the literature have been reported from Indi...

In 68 patients with anorectal malformations cardiovascular anomalies (CVA) were seen in 15 and genitourinary (GU) anomalies in 30. CVA were more frequent (33%) whenever there was a GU anomaly. Ventricular septal defect was the most frequent lesion. All but 1 CVA occurred with type III anorectal malformation. The complexity of the cardiac lesion did not parallel that of the GU anomaly.

(This section is meant for residents to check their understanding regarding a particular topic) QUESTIONS 1. What are the various types of anorectal malformations (ARM)? 2. What is the pathophysiology of ARM? 3. What are the clinical features of newborn with anorectal malformation? 4. What are the radiological investigations required for diagnostic evaluation? 5. What are its associated anomalies?