Defective enamel formation is the defects occurring at the stages of enamel formation. Amelogenesis imperfect (AI) is a hereditary disorder that causes developmental disturbances in the structure of enamel. Quantitative defects in matrix formation leads to hypoplastic form of Amelogenesis imperfecta. Inadequate mineralization of matrix leads to hypocalcification and hypomaturationvariants. It i...

Amelogenesis imperfecta has been defined as a group of hereditary enamel defects which may or may not be associated with some other dental and skeletal developmental defects. It can be characterized by enamel hypoplasia, hypomaturation, or hypo-calcification of the teeth. This clinical report describes the oral rehabilitation of a twenty two year old female patient with amelogenesis imperfecta ...

An interdisciplinary approach can be used to treat the uncommon hereditary defect known as amelogenesis imperfecta, which ischaracterised by insufficient crown length, hypersensitivity, dental caries, and decreased vertical dimension. The present case reportdescribes a successfully managed of imperfecta with full mouth rehabilitation using implant supported prosthesis. This helped restore funct...

Numerous cases of enamel renal syndrome have been previously reported. Various terms, such as enamel renal syndrome, amelogenesis imperfecta and gingival fibromatosis syndrome, and enamel-renal-gingival syndrome, have been used for patients presenting with the dental phenotype characteristic of this condition, nephrocalcinosis or nephrolithiasis, and gingival findings. This report describes a c...

Teeth fragments from members of a family clinically and genetically diagnosed as having amelogenesis imperfecta were studied by scanning electron microscopy and X-ray microprobe analysis to establish the morphological patterns and the quantitative concentration of calcium in the enamel of anterior (canine, incisor) and posterior (premolar and molar) teeth. The prism patterns in the enamel of te...

Kohlschütter-Tönz Syndrome is a rare disorder clinically characterized by amelogenesis imperfecta, epilepsy and progressive mental deterioration. We present an additional case of this syndrome of a nine year-old boy who was referred by pigmented teeth. The mental deterioration was associated with speech delay, impulsive behavior, attention-deficit/hyperactivity disorder, and learning problems. ...

Amelogenesis imperfecta is a term for a clinically and genetically heterogeneous group of conditions that affect the dental enamel. This paper reports a case of Amelogenesis Imperfect managed by composite veneers.

Amelogenesis imperfecta is a group of genetic disorders that affects both the morphology and quality of tooth structure. Although the disease entity is primarily associated with abnormalities of dental and oral structures, it has been reported to be associated with a few syndromes. A 9-year-old girl with minor thalassemia referred to the Department of Pediatric Dentistry of the Mashhad Faculty ...

OBJECTIVES The purpose of this study was to use quantitative x-ray microprobe analysis with scanning electron microscopy to define the morphostructural and calcification patterns in the enamel of teeth with the hypomineralized variant of amelogenesis imperfecta. STUDY DESIGN We compared 5 fragments of permanent human canines from patients with clinically diagnosed hypomineralized amelogenesis...