Scimitar vein is the partial anomalous pulmonary venous connection usually draining lower pulmonary lobe to the inferior vena cava or right atrium. We present a scimitar vein anomaly in a 34-year-old woman with the uncommon association of a secundum type of atrial septal defect and atretic right upper pulmonary vein. She presented with increasing dyspnea for 2 months, however, she was asymptoma...

Partial anomalous pulmonary venous return (PAPVR) is a congenital anomaly in which one or more, but not all, of the pulmonary veins are connected to a systemic vein or to the right atrium directly. Its incidence is higher in autopsy series than in clinical series. We report 51 cases of PAPVR diagnosed by cardiac catheterization and evaluated from the aspects of age, sex, type and associated ano...

In t roduct ion Internal jugular vein (LJV) phlebectasia is a rare form of congenital venous anomaly. Less than 50 cases have been reported in the literature world-wide. In the majority of cases the lesion was in boys and on the right side. It is a fusiform dilation of the vein without any apparent ob­ struction, and is believed to be due to congenital thinning of the vessel wall. It can mimic ...

Klippel-Trénaunay syndrome (KTS) is a rare vascular congenital anomaly affecting less than 200,000 people in the United States. Vascular malformations associated with KTS tend to affect slow flow systems: venous, capillary, and lymphatic systems. The nature of the syndrome leads to a higher risk for the development of arteriovenous malformations. Our case presentation describes a patient with K...

Vascular anomalies are a heterogeneous group of congenital blood vessel disorders more typically referred to as birthmarks. Subcategorized into vascular tumors and malformations, each anomaly is characterized by specific morphology, pathophysiology, clinical behavior, and management approach. Hemangiomas are the most common vascular tumor. Lymphatic, capillary, venous, and arteriovenous malform...

Echocardiography revealed systemic artery to pulmonary venous fistula, a rare vascular anomaly, in a 20-month-old girl, and multislice computed tomography angiography (CTA) was performed to rule out congenital heart disease. Normal bronchial connection and pulmonary vasculature were observed in the lung. The fistula drained through the left inferior pulmonary vein to the left atrium leading to ...

Haemobilia or bleeding into the biliary tract is a very rare occurrence in children. We report an infant who bled profusely into the biliary tract from dilated pericholecystic veins that were part of a sponge like mass of tortuous, collateral veins replacing the portal vein. This venous anomaly is referred to as cavernous transformation of the portal vein or portal cavernoma and is a sequel of ...

FRIEDLOWSKY, in 1868, was the first to report total anomalous pulmonary venous connection.' 2 This entity, with its, multiple varieties,3 is receiving increasing attention with the recent encouraging reports of suecessful surgical therapy.4 The infradiaphragmatic form was first described by Ghon in 1916,5 and a total of 37 cases has since been reported.5 24 Obstruction to the pulmonary venous d...

INTRODUCTION Peters anomaly is a rare developmental malformation involving the anterior segment of the eye, which culminates in amblyopia or congenital blindness. Multiple ocular and/or systemic malformations have been observed with this anomaly, and novel comorbidities continue to be reported. CASE PRESENTATION The probands were monozygotic twin boys (twin I and twin II) born to consanguineo...

Inferior sinus venosus arterial septal defect (ASD) is a rare congenital cardiac anomaly. As with other types of ASDs and patent foramen ovale (PFO), this results in arteri-venous shunting the risk developing paradoxical embolism (PDE) to systemic circulation from venous emboli. We report case 67-year-old lady presented emergency department (ED) massive pulmonary (PE) recurrent acute limb ischa...