نتایج جستجو برای: type 1 tyrosinemia

تعداد نتایج: 3647237  

Journal: :Journal of hepatology 1986
D H Van Thiel L M Gartner F K Thorp S L Newman J A Lindahl E Stoner M I New T E Starzl

The clinical history before transplantation and subsequent clinical and biochemical course of 3 children and one adult with hereditary tyrosinemia treated by orthotopic hepatic transplantation is described. All four patients are now free of their previous dietary restrictions and appear to be cured of both their metabolic disease and their hepatic neoplasm.

Journal: :گوارش 0
mehri najafi-sani hamidreza kianifar seyed mohammadmehdi mir-nasseri ahmad khodadad

background: there are only a very small number of reports which discuss subtype, sex distribution, clinical features and laboratory characteristics of autoimmune hepatitis in children. the aim of this study was both to define the clinical features, biochemical and histological findings and also to determine the age and sex related distribution of autoimmune hepatitis (aih). materials and method...

Journal: :The Southeast Asian journal of tropical medicine and public health 2003
Hye-Ran Yoon Kyung Ryul Lee Hohyun Kim Seungwoo Kang Yunmi Ha Dong Hwan Lee

Seoul Clinical Laboratories began screening newborns and high risk group blood spots with tandem mass spectrometry (MS/MS) in April 2001. The goal was to determine approximate prevalence of metabolic disorders and optimization of decision criteria for estimation of preventive effect with early diagnosis. Approximately 44,300 neonates and children were screened and the estimated prevalence (newb...

Journal: :Genes & development 2015
Kirk J Wangensteen Sophia Zhang Linda E Greenbaum Klaus H Kaestner

The fundamental question of which genes are most important in controlling liver regeneration remains unanswered. We employed a parallel screen to test the impact of 43 selected genes on liver repopulation in the Fah(-/-) mouse model of hereditary tyrosinemia. We discovered that the transcription factor Foxa3 was a strong promoter of liver regeneration, while tumor necrosis factor receptor 1 (TN...

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