A nomenclature is described for congenital heart disease employing sequential chamber localization. It is an eclectic system based in part upon the previous classifications of Van Praagh and Kirklin. It links together the atrial, ventricular, and arterial segments of the heart and then permits tabulation of associated anomalies. The atrial segment of the heart can exist as situs solitus, situs ...

gut, resulting from the shift to the right side, of tissue derived from the left side of the embryo. Rightness and leftness of derivation are maintained and can be observed in later development when these regions have been stained. When stain was localized in the right wall of the duodenum after application to the right or midventral region in the level of the prospective duodenum, or posterior...

a Serviço Diagnóstico por Imagem, Hospital Particular de Viana do Castelo, Viana do Castelo, Portugal e Serviço de Imagiologia, Clínica Girassol, Luanda, Angola b Serviço de Cardiologia Pediátrica, Hospital da Cruz Vermelha, Lisboa, Portugal e Serviço de Cardiologia Pediátrica, Clínica Girassol, Luanda, Angola c Serviço de Cardiologia, Hospital Militar Principal de Luanda, Luanda, Angola d Serv...

Dextrocardia associated with atrial situs solitus is commonly referred to as dextroversion. Dextroversion is a result of early interruption of normal embryological development and, therefore, rarely occurs without other associated cardiac and noncardiac anomalies. While percutaneous coronary intervention has been described in many cases of dextrocardia with situs inversus, it has not been previ...

Laterality defects in humans, situs inversus and heterotaxy, are rare disorders, with an incidence of 1:8000 to 1:10 000 in the general population, and a multifactorial etiology. It has been proved that 1.44/10 000 of all cardiac problems are associated with malformations of left-right asymmetry and heterotaxy accounts for 3% of all congenital heart defects. It is considered that defects of sit...

We report a rare case of a female patient with situs inversus totalis. She developed cholelithiasis which was diagnosed on abdominal ultrasound and she underwent laparoscopic cholecystectomy for the left sided gall bladder. The literature on this subject is reviewed. We want to highlight the important aspects of the management in such rare scenario.

Total transection of the retrohepatic inferior vena cava from blunt trauma is a rare and usually fatal injury. Such an injury in a patient with total situs inversus and previous surgical correction of great vessel transposition is described. A possible mechanism for the injury is suggested.

Situs inversus totalis in the pediatric population is a rare laterality defect characterized by a complete mirror-image reversal of the normal anatomy. The association with hepatic malignancies has been rarely described in the literature. Because of the complex anatomy, multidisciplinary approach and adequate pre-operative planning are crucial in order to understand the hepatic anatomy.

A healthy, non-consanguineous couple had a son with complete situs inversus viscerum (including dextrocardia but without other cardiac defects), broad thumbs and big toes, postaxial polydactyly, average intelligence and length proportion of the extremities, and a normal face. The common cause of these defects may have a role in the origin of sidedness and symmetry in morphogenesis.