PURPOSE This study evaluated the clinical manifestations of and risk factors for pituitary insufficiency in children and adolescents with Rathke's cleft cysts. METHODS Forty-four patients with Rathke's cleft cysts younger than 19 years who visited Seoul National University Children's Hospital between January 1995 and September 2009 were enrolled. Rathke's cleft cysts were confirmed histologic...

The case of a 5-month-old black female child with a linear sebaceous naevus syndrome and multiple congenital anomalies is presented. Ocular malformations consisted of colobomatous changes of the lid and retina, dermoid of the conjunctiva, chorioretinal changes, and peripapillary atrophy of the optic nerve. Systemic findings included midline cleft of the secondary palate with involvement by the ...

we report five cases of duplicated external ear canal with especial attention to its histology and surgical care of facial nerve for their complete resection. these five patients were selected from 50 cases of first bronchial cleft anomalies including atretic external ear canals, preauricular fistula, cyst and sinuses. the characteristic histopathology and clinical features such as external ope...

In this article, we report a rare case of a cervical cystic vagal schwannoma mimicking a type 3 second branchial cleft cyst clinically, radiologically and cytologically. Although schwannoma is rare, it should be considered in the differential diagnosis of cystic neck masses. This article suggests that Doppler ultrasonography, computed tomography and fine needle aspiration biopsy findings may no...

Teratoma of oropharyngeal region, also known as an epignathus, is found in approximately 1:35,000– 1:200,000 live births with female predominance.[1] Congenital malformations such as cleft palate, bifid tongue, dorso-nasal fistula and nasal dermoid cyst may be associated with teratoma of oropharyngeal region in 6 % cases.[2] Management of these cases are challenging with respect to handling of ...

Management of a neonate with cleft lip and palate and assuring the parents regarding the future well being of the child can be a challenging task. Timely referral by pediatrician and treatment by an Orthodontist and a Plastic Surgeon can help in limiting the deformity to its minimum and aid in normal growth and development of the child. This paper describes the treatment of two neonates with un...

OBJECTIVES The aim of this study was to compare nostril height, width, collumelar length, interalar distance and nostril symetry between unilateral complete cleft lip/palate patients undergoing nasoalveolar moulding (NAM) and incomplete cleft lip patients/palate with no need of presurgical moulding before and after cheiloplasty with primary nasal correction. Our study group included 18 patients...