We previously reported that pulmonary artery pressures can be assessed in children with chronic rheumatic mitral valve disease by measuring right maximum spatial vector from Frank vectorcardiogram. To simplify the calculation, pulmonary artery systolic pressure was correlated with maximum negative deflection on Frank scalar X-lead (SX), maximum negative deflection on scalar Z lead (SZ), sum tot...

introduction:  in patients who underwent surgery to repair tetralogy of fallot, right ventricular dilation from pulmonary regurgitation may be result in right ventricular failure, arrhythmias and cardiac arrest. hence, pulmonary valve replacement may be necessary to reduce right ventricular volume overload. the aim of present study was to assess the effects of pulmonary valve replacement on rig...

BACKGROUND Transcatheter balloon valvuloplasty has been the accepted first line treatment for congenital pulmonic stenosis (PS) in children. Transcatheter closure of perimembranous ventricular septal defect (VSD) with Amplatzer VSD occluder is an alternative to surgical repair. CASE PRESENTATION A 12 year old boy presented with history of exertional dyspnea and atypical chest pain. Physical f...

The Noonan syndrome is a rare disorder, one of whose major complications is cardiovascular involvement. A wide spectrum of congenital heart diseases has been observed in this syndrome. The most common cardiac disorder is pulmonary valve stenosis, which has a progressive nature. Hypertrophic cardiomyopathy is less common, but its morbidity and mortality rates are high. We herein introduce a 12-y...

Objective: We aimed to retrospectively evaluate the clinical, demographic, clinical and echocardiographic findings of children diagnosed with chest deformity in pediatric cardiology clinic.
 Material Method: This study enrolled under age 18 years who were referred our unit, over a period six (January 2017-December 2022).
 Results: The mean patients was 9.9 ± 5.2 years, median 11 (0-18...

BACKGROUND The patency of foramen ovale (FO) in fetal circulation is very important, and premature closure of FO could be associated with several pathological conditions. METHODS We report a patient in whom premature closure of FO in fetal life was associated with late clinical onset of mitral valve stenosis and subsequent development of irreversible pulmonary hypertension (PH). RESULTS The...

Echocardiographic examination in a patient with primary pulmonary hypertension demonstrated midsystolic closure of the aortic valve, which has often been described in hypertrophic cardiomyopathy with or without obstruction, in discrete subaortic stenosis, and in ruptured aneurysm of the right coronary sinus of Valsalva. A possible mechanism for this finding in primary pulmonary hypertension and...

We describe the case of a 54-year-old female with severe aortic stenosis and a background of severe comorbidities including prior radiotherapy for Hodgkin’s lymphoma, splenectomy, severe chronic obstructive pulmonary disease, scleroderma with laryngeal and esophageal involvement, and systemic and pulmonary hypertension. The patient underwent totally video-guided aortic valve replacement through...

Among 166 specimens with classical complete transposition, pulmonary or subpulmonary stenosis was present in 22 cases. The bases for obstruction were pulmonary valvular stenosis (one case), membranous subpulmonary stenosis (nine cases), anomalous attachment of the mitral valve to the ventricular septum (five cases) and combinations of causes (seven cases). Conditions contributing to combination...

BACKGROUND Surgical and transcatheter bioprosthetic valves (BPVs) in the pulmonary position in patients with congenital heart disease may ultimately fail and undergo transcatheter reintervention. Angiographic assessment of the mechanism of BPV failure has not been previously described. AIMS The aim of this study was to determine the mode of BPV failure (stenosis/regurgitation) requiring trans...