Intrathecal paragangliomas are an unusual cause of the cauda equina syndrome. Although well documented in the neuropathology and neurosurgery literature, only one case report has appeared in the radiology literature to date [1]. Recognition of the tumor is important because of its biologic characteristics ; which differ significantly from ependymoma, the tumor with which it is most commonly con...

1 Resident Physician, Hospital Paulista de Otorrinolaringologia. 2 Ph.D., Professor, UNIFESP-EPM. 3 Post-graduate studies under course, Discipline of Otorhinolaryngology, Escola Paulista de Medicina. 4 Otorhinolaryngologist. Study conducted at Hospital Paulista de Otorrinolaringologia. Address correspondence to: Doutor José Ricardo Gurgel Testa – Rua Doutor Diogo de Faria 780 Sao Paulo SP 04037...

tions that may result in disfigurement and functional impairment. Other manifestations of the syndrome include neuroendocrine tumors of the duodenum (somatostationomas) and pheochromocytomas. Numerous mapping studies localized the NFl gene on the long arm of chromosome 17 near the centromere and led to cloning of the complete coding region (13). The NFl gene encodes an mRNA of 11-13 kb containi...

Paragangliomas of the head and neck are rare especially in larynx. A 36 year old female patient presented with a history progressive voice change difficulty swallowing for 6 months. During endoscopic examinationsmooth surfaced mass on Left supraglottic region, was noted. Tumour excised through transcervical excision. Histology immunohistochemistry tumour revealed that, it paraganglioma.

Paragangliomas of urinary bladder are extremely rare which usually present with characteristic clinical picture in about half of the cases. We report a case where the presentation was unusual, leading to initial misdiagnosis corrected on histological review.

BACKGROUND AND PURPOSE Paragangliomas are tumors of neural crest origin commonly arising from the carotid body, vagal nerve, or jugular bulb. The definitive treatment for these tumors is surgical resection, often augmented with pre-operative embolization due their highly vascular nature. We present our experience examining the efficacy and safety of endovascular embolization of these rare tumor...

Pheochromocytomas and paragangliomas are catecholamine-secreting tumors of neural crest origin that arise from the adrenal medulla or extra-adrenal sympathetic paraganglia, respectively. Over the last decade, the extensive genetic heterogeneity of these tumors came to light with the identification of multiple susceptibility genes. These mutations account for at least one-third of pheochromocyto...

Paragangliomas are extra-adrenal tumors of the autonomic nervous system and may be found within the skull base, neck, mediastinum and periaortic region. Paragangliomas of the urinary bladder are rare, and non-functioning bladder paraganglioma is even rarer and not easily recognized. Histological examination is often key in leading to a definitive diagnosis. The current report presents a case of...

Spinal paragangliomas are very rare neuroendocrine tumors often presenting with low back pain and radicular symptoms; once resected, they often show benign clinical outcomes. Radiographically spinal paragangliomas mimic more commonly described tumors, such as ependymomas, schwannomas, meningiomas, and even hemangiomas, but a "salt and pepper" appearance related to a serpiginous vascular structu...

BACKGROUND Little is known about management and prognosis for malignant head & neck paragangliomas. We reviewed records of these patients to determine optimal treatment strategies. METHODS We reviewed 113 cases of head & neck paragangliomas treated at our institution from 1970 to 2005. Nineteen patients were included in the study. All had primary surgical treatment at another institution. Met...