Granulomatosis with polyangiitis (Wegener's granulomatosis) is one of the anti-neutrophil cytoplasmic anti-body-associated small vessel vasculitides. Upper and lower respiratory system and kidneys are most commonly affected. The disease is characterized by granulomatous inflammation of the respiratory tract and necrotizing vasculitis of small to medium-sized blood vessels. Most patients show in...

Skull base osteomyelitis in the setting of granulomatosis with polyangiitis (GPA) is rare and entails significant diagnostic challenges. We present a case of a 65-year-old Caucasian man with a history of rheumatoid arthritis, off immunosuppression for 18 months, who presented with 2 years of chronic headaches, severe fatigue, saddle nose deformity and 20-kilogram unintentional weight loss. Maxi...

A 5-year-old boy and his father with Pfeiffer syndrome are described. They had acrocephaly, hypertelorism, antimongoloid slant of the palpebral fissures, protrusion of the eyes, large and broad nose, small mandible, irregularly placed teeth, additional upper canine, high-arched palate, partial syndactyly of fingers and toes, brachydactyly of toes, valgus deformity of hypertrophied triangular gr...

Frontoethmoidal encephaloceles are herniations of the intracranial contents through a defect in the skull at the junction of the frontal and ethmoidal bones. They are generally classified as nasofrontal, nasoethmoidal, and naso-orbital, although there may be some overlap or multiplicity. The records of 35 patients treated for frontoethmoidal encephaloceles were examined. Of these, 12 cases with...

The unilateral cleft lip is a complex deformity. Surgical correction has evolved from a straight repair through triangular and quadrilateral repairs to the Rotation Advancement Technique of Millard. The latter is the technique followed at our centre for all unilateral cleft lip patients. We operate on these at five to six months of age, do not use pre-surgical orthodontics, and follow a protoco...

OBJECTIVE The aim of this study is to use porous high-density polyethylene grafts (Medpor) in open rhinoplasty and then assess complication rate and aesthetic outcomes. METHODS In a prospective cohort study, we performed open rhinoplasty and employed Medpor as rhinoplasty grafts. Then we compared their complication rate. RESULTS In a total of 64 patients, 84 Medpor grafts--8 dorsal grafts, ...

Local anaesthesia is increasingly being used for nasal manipulation. Doubt remains over the discomfort associated with this procedure. We studied in a prospective manner, the acceptability and effectiveness of nasal manipulation with intravenous sedation and local anaesthesia, in a case series of thirty-five patients. Patients used linear analogue scales to assess outcome and pain associated wi...

anthropometry, a useful method for evaluating craniofacial soft tissues, makes the quantitative description of the face possible. it also assesses the degree of disharmony and imbalance in the growth and development of the face. the aim of this study was to examine the overall common age-related changes of nasomaxillary complex of adolescent boys in northeast iran. three- hundred- twelve 12 to ...

Rhinophyma may have been first recognized in ancient Greece and Arabia.1,2 Elliott et al. and Matton et al. credit Hebra with naming the disease in the mid-nineteenth century.3,4 The name is derived from the Greek rhis, for nose, and phyma, meaning growth. Many imaginative terms have been used to describe the erythematous, hypertrophied, and inflamed nose that typifies rhinophyma. In the past, ...

The management of nasal deformities especially after rhinoplasty is a challenge. Postsurgical edema may last 6-8 months, causing aesthetic irregularities and nose deformities. The aim of this study is to present the correction of minor nose deformities secondary to rhinoplasty using hyaluronic acid subdermal injections. Eleven patients were treated between 2009 and 2011 with subdermal injection...